On the possible role of muscle in the pathogenesis of spinal muscular atrophy

Fundamental and Clinical Pharmacology

Volumn 15, Issue 1, 2001, Pages 31-40

  Guettier Sigrist, Séverine ^a   Coupin, Gilliane ^a   Braun, Serge ^b   Rogovitz, David ^a   Courdier, Isabelle ^a   Warter, Jean Marie ^c   Poindron, Philippe ^a  

^a UNIVERSITÉ DE STRASBOURG   (France)

^b TRANSGENE S A   (France)

^c UNIVERSITY HOSPITAL OF STRASBOURG   (France)

Author keywords

Motor neurons; Muscle cells; Myf 5; Nerve muscle coculture; Spinal muscle atrophy; Survival motor neuron

Indexed keywords

MYOGENIC FACTOR 5; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG;

ADOLESCENT; ARTICLE; CELL SURVIVAL; CHROMOSOME 5Q; CONTROLLED STUDY; EMBRYO; FETUS; GENE DELETION; GENE ISOLATION; HUMAN; HUMAN CELL; HUMAN TISSUE; MOTONEURON; MUSCLE DEVELOPMENT; PATHOGENESIS; PRIORITY JOURNAL; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SATELLITE CELL; SCHOOL CHILD; SPINAL MUSCULAR ATROPHY;

ANIMALS; CELL FUSION; CELL SURVIVAL; CELLS, CULTURED; COCULTURE TECHNIQUES; CYCLIC AMP RESPONSE ELEMENT-BINDING PROTEIN; DISEASE MODELS, ANIMAL; GENE DELETION; HUMANS; MOTOR NEURONS; MUSCLE, SKELETAL; MUSCULAR ATROPHY, SPINAL; NERVE DEGENERATION; NERVE TISSUE PROTEINS; RATS; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; RNA-BINDING PROTEINS; TRANSCRIPTION FACTORS;

EID: 0035036019     PISSN: 07673981     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1472-8206.2001.00006.x     Document Type: Article

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