Congenital surfactant protein B deficiency - Emphasis on imaging

Pediatric Radiology

Volumn 31, Issue 5, 2001, Pages 327-331

  Newman, B ^a   Kuhn, Jerald P ^b   Kramer, Sandra S ^c   Carcillo, Joseph A ^a  

^a CHILDREN S HOSPITAL OF PITTSBURGH   (United States)

^b CHILDREN S HOSPITAL OF BUFFALO   (United States)

^c CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

SURFACTANT PROTEIN B;

ARTICLE; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; CONGENITAL DISORDER; CONTROLLED STUDY; DIAGNOSTIC IMAGING; DNA DETERMINATION; FEMALE; FIBROSIS; HUMAN; LUNG ALVEOLUS PROTEINOSIS; LUNG LAVAGE; MALE; MEDICAL INFORMATION; NEONATAL RESPIRATORY DISTRESS SYNDROME; NEWBORN; PRIORITY JOURNAL; PROTEIN DEFICIENCY; SPIRAL COMPUTER ASSISTED TOMOGRAPHY; THORAX RADIOGRAPHY;

EXTRACORPOREAL MEMBRANE OXYGENATION; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; MALE; MUTATION; PROTEIN PRECURSORS; PROTEOLIPIDS; PULMONARY ALVEOLAR PROTEINOSIS; TOMOGRAPHY, X-RAY COMPUTED;

EID: 0035025256     PISSN: 03010449     EISSN: None     Source Type: Journal    
DOI: 10.1007/s002470100438     Document Type: Article

References (16)

1. Brief report: Deficiency of pulmonary surfactant protein B in congenital alveolar proteinosis
2. Surfactant protein B deficiency: Insights into inherited disorders of lung cell metabolism
3. A mutation in the surfactant protein B gene responsible for fatal neonatal respiratory disease in multiple kindreds
4. Molecular and phenotypic variability in the congenital alveolar proteinosis syndrome associated with inherited surfactant protein B deficiency
5. Transient surfactant protein B deficiency in a term infant with severe respiratory failure
6. Neonatal respiratory distress in near-term infants-consider surfactant protein B deficiency
7. Surfactant protein B deficiency: Radiographic manifestations
8. Surfactant protein genes and human disease: The plot thickens
9. Synthetic protein analogues in artificial surfactants
10. Neonatal respiratory disease due to surfactant protein B deficiency
11. Surfactant protein-B deficiency
12. Lung transplantation for treatment of infants with surfactant protein B deficiency
13. Lack of GM-CSF as a cause of pulmonary alveolar proteinosis
14. Human pulmonary alveolar proteinosis associated with a defect in GM-CSF/IL-3/IL-5 receptor common chain expression
15. CT scan patterns of pulmonary alveolar proteinosis in children