Mitochondrial respiratory chain deficiency revealed by hypothermia

Neuropediatrics

Volumn 32, Issue 2, 2001, Pages 104-106

  Cholley, Florence ^a   Edery, P ^a   Ricquier, D ^b   Peudenier, S ^c   Slama, A ^a   Tardieu, Marc ^a  

^a BICÊTRE HOSPITAL   (France)

^b CEREMOND/CNRS   (France)

^c SERVICE DE RHUMATOLOGIE   (France)

Author keywords

Hypothermia; Respiratory chain dysfunction; Uncoupling proteins

Indexed keywords

UNCOUPLING PROTEIN;

ARTICLE; BONE LESION; BROWN ADIPOSE TISSUE; CASE REPORT; CORNEA DISEASE; FEMALE; GROWTH RETARDATION; HUMAN; HUMAN TISSUE; HYPERLACTATEMIA; HYPOTHERMIA; MUSCLE MITOCHONDRION; POLAROGRAPHY; PRESCHOOL CHILD; PRIORITY JOURNAL; RESPIRATORY CHAIN; RESPIRATORY CHAIN DEFICIENCY; SPECTROPHOTOMETRY; THERMOGENESIS;

BIOPSY; CARRIER PROTEINS; CHILD, PRESCHOOL; CYTOCHROME-C OXIDASE DEFICIENCY; ELECTRON TRANSPORT COMPLEX III; FEMALE; FRACTURES, SPONTANEOUS; HUMANS; HYPOTHERMIA; INFANT; INFANT, NEWBORN; ION CHANNELS; MITOCHONDRIAL MYOPATHIES; MITOCHONDRIAL PROTEINS; MUSCLE, SKELETAL; RETINITIS PIGMENTOSA; RNA, MESSENGER;

EID: 0034997172     PISSN: 0174304X     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2001-13878     Document Type: Article

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