Muscle plasma membrane changes in dystrophin gene exon 52 knockout mouse

Pathology Research and Practice

Volumn 197, Issue 6, 2001, Pages 441-447

  Shibuya, Seiji ^a   Wakayama, Yoshihiro ^a   Murahashi, Makoto ^a   Kojima, Hiroko ^a   Oniki, Hiroaki ^a   Matsuzaki, Tetsuya ^b   Nonaka, Ikuya ^b  

^a SHOWA UNIVERSITY FUJIGAOKA HOSPITAL   (Japan)

^b NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

Author keywords

Dystrophin gene; Exon 52; Knockout mouse; MDX mouse; Muscle plasma membrane

Indexed keywords

DYSTROPHIN;

ADOLESCENT; AGE; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DENSITY; EXON; EXTENSOR DIGITORUM LONGUS MUSCLE; FREEZE FRACTURE; KNOCKOUT MOUSE; MOUSE; NONHUMAN; PARTICLE SIZE; SARCOLEMMA;

EID: 0034973728     PISSN: 03440338     EISSN: None     Source Type: Journal    
DOI: 10.1078/0344-0338-00058     Document Type: Article

References (26)

1. Structure and mutation of the dystrophin gene
2. Preservation of the C-terminus of dystrophin molecule in the skeletal muscle from Becker muscular dystrophy
3. Targeted disruption of exon 52 in the mouse dystrophin gene induced muscle degeneration similar to that observed in Duchenne muscular dystrophy
4. Freeze-fracture studies of muscle caveolae in human muscular dystrophy
5. Deficiency of a glycoprotein component of the dystrophin complex in dystrophic muscle
6. Expression of aquaporin-4 in fast-twitch fibers of mammalian skeletal muscle
7. Dystrophin: The protein product of the Duchenne muscular dystrophy locus
8. Changes in number and distribution of orthogonal arrays during postnatal muscle development
9. Immunocytochemical studies of aquaporin 4 in the skeletal muscle of mdx mouse
10. Caveolin-3 associates with developing T-tubules during muscle differentiation
11. Further aspects of muscular dystrophy in mdx mice
12. Mdx mice show progressive weakness and muscle deterioration with age
13. Forced expression of dystrophin deletion constructs reveals structure-function correlations
14. Direct immunogold labeling of aquaporin 4 in square arrays of astrocyte and ependymocyte plasma membranes in rat brain and spinal cord
15. Increased number of caveolae and caveolin-3 overexpression in Duchenne muscular dystrophy
16. Duchenne dystrophy alteration in muscle plasma membrane structure
17. Freeze-fracture studies of myofiber plasma membrane in X chromosome-linked muscular dystrophy (mdx) mice
18. The molecular basis of muscular dystrophy in the mdx mouse: A point mutation
19. Skeletal muscle pathology in X chromosome-linked muscular dystrophy (mdx) mouse
20. Increased caveolin-3 levels in mdx mouse muscles
21. Absence of orthogonal arrays in kidney, brain and muscle from transgenic knockout mice lacking water channel aquaporin-4
22. Duchenne dystrophy reduced density of orthogonal array subunit particles in muscle plasma membrane
23. Quantitative freeze-fracture electron-microscopic analysis of muscle plasma membrane of bupivacaine-induced myopathy
24. Dystrophin immunostaining and freeze-fracture studies of muscles of patients with early stage amyotrophic lateral sclerosis and Duchenne muscular dystrophy
25. Immunoreactivity of antibodies raised against synthetic peptide fragments predicted from mid portions of dystrophin cDNA
26. Freeze fracture analysis of muscle plasma membrane in bupivacaine HCL-induced degeneration and regeneration