Cognitive deficits associated with a recently reported familial neurodegenerative disease: Familial encephalopathy with neuroserpin inclusion bodies

Archives of Neurology

Volumn 58, Issue 9, 2001, Pages 1429-1434

  Bradshaw, Charles B ^a   Davis, Richard L ^a   Shrimpton, Antony E ^a   Holohan, Peter D ^a   Rea, Cornelia B ^b   Fieglin, David ^a   Kent, Paul ^a   Collins, George H ^a  

^a State University of New York Upstate Medical University: College of Medicine   (United States)

^b STATE UNIVERSITY OF NEW YORK   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ADULT; AGED; ARTICLE; AUTOSOMAL DOMINANT DISORDER; CLINICAL ARTICLE; COGNITIVE DEFECT; DEGENERATIVE DISEASE; DEMENTIA; DIAGNOSTIC IMAGING; DISEASE ASSOCIATION; DISEASE SEVERITY; ELECTROENCEPHALOGRAM; FAMILIAL DISEASE; FAMILIAL ENCEPHALOPATHY WITH NEUROSERPIN INCLUSION BODIES; FEMALE; GENE MUTATION; HUMAN; HUMAN TISSUE; MALE; MEMORY; NEUROLOGIC DISEASE; NUCLEAR MAGNETIC RESONANCE IMAGING; PRIORITY JOURNAL; RECALL; SINGLE PHOTON EMISSION COMPUTER TOMOGRAPHY;

EID: 0034857852     PISSN: 00039942     EISSN: None     Source Type: Journal    
DOI: 10.1001/archneur.58.9.1429     Document Type: Article

References (22)

1. Alzheimer's disease and other dementing disorders
2. What happens when mutant neuroserpins get into bad shape
3. Familial encephalopathy with neuroserpin inclusion bodies
4. Familial dementia caused by a polymerization of mutant neuroserpin
5. Studies of interference in serial verbal reactions
6. Attention, confusional states and neglect
7. Letter and category fluency in patients with frontal lobe lesions
8. Parkinson's disease
9. Neuropsychological functioning in Alzheimer's disease
10. Clinical characteristics of a chromosome 17-linked rapidly progressing familial frontotemporal dementia
11. Localization of disinhibition dementia parkinsonism amotrophy complex to 17q21-22
12. Localization of the gene for rapidly progressive autosomal dominant parkinsonism and dementia with pallido-pontonigral degeneration to chromosome 17q21
13. Familial progressive gliosis: Presence of prions and linkage to chromosome 17
14. Neuroserpin mutation S52R causes neuroserpin accumulation in neurons and is associated with progressive myoclonus epilepsy
15. An autosomal dominant epilepsy with dementia and intraneuronal inclusion bodies
16. Collins bodies and atypical myoclonus bodies: The neuroserpin connection