Defects of type I procollagen metabolism correlated with decrease of prolidase activity in a case of lethal osteogenesis imperfecta

European Journal of Biochemistry

Volumn 268, Issue 7, 2001, Pages 2172-2178

  Galicka, Anna ^a   Wolczyñski, Slawomir ^a   Anchim, Tomasz ^a   Surazyñski, Arkadiusz ^a   Lesniewicz, Ryszard ^a   Palka, Jerzy ^a  

^a MEDICAL UNIVERSITY OF BIALYSTOK   (Poland)

Author keywords

Collagen; Osteogenesis imperfecta; Prolidase

Indexed keywords

BETA1 INTEGRIN; DNA; ENZYME; PROCOLLAGEN; PROLINE DIPEPTIDASE; SOMATOMEDIN C RECEPTOR;

ARTICLE; CASE REPORT; CELL CULTURE; CELL GROWTH; CELL SECRETION; COLLAGEN DEGRADATION; COLLAGEN METABOLISM; COLLAGEN SYNTHESIS; CONTROLLED STUDY; DISEASE SEVERITY; DNA SYNTHESIS; ENZYME ACTIVITY; ENZYME REGULATION; FETUS; HUMAN; HUMAN CELL; MALE; OSTEOGENESIS IMPERFECTA; PERINATAL PERIOD; PRIORITY JOURNAL; PROTEIN EXPRESSION; SKIN FIBROBLAST;

ADULT; ANTIGENS, CD29; CELLS, CULTURED; CHILD; COLLAGEN; DIPEPTIDASES; DNA REPLICATION; ELECTROPHORESIS, POLYACRYLAMIDE GEL; FEMALE; FIBROBLASTS; HUMANS; INFANT, NEWBORN; INSULIN-LIKE GROWTH FACTOR I; MALE; OSTEOGENESIS IMPERFECTA; PROCOLLAGEN; RECEPTOR, IGF TYPE 1;

EID: 0034843268     PISSN: 00142956     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1432-1327.2001.02099.x     Document Type: Article

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