Oxidation of galactose by galactose-1-phosphate uridyltransferase-deficient lymphoblasts

Journal of Inherited Metabolic Disease

Volumn 24, Issue 4, 2001, Pages 465-476

  Yager, C ^a,b   Gibson, J ^a,c   States, B ^a,b   Elsas, L J ^a,d   Segal, S ^a,b  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^c ARKANSAS CHILDREN S HOSPITAL   (United States)

^d EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CARBON 14; CARBON DIOXIDE; GALACTOSE; GALACTOSE 1 PHOSPHATE URIDYLYLTRANSFERASE; GLUCOSE; SUGAR;

ADOLESCENT; ADULT; ARTICLE; CELL LINE; CHILD; CLINICAL ARTICLE; CONCENTRATION RESPONSE; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME ANALYSIS; ENZYME DEFICIENCY; EPSTEIN BARR VIRUS; GALACTOSEMIA; GENE DELETION; GENE MUTATION; GENOTYPE; HOMOZYGOSITY; HUMAN; HUMAN CELL; LYMPHOBLAST; LYMPHOCYTE TRANSFORMATION; OXIDATION;

ADOLESCENT; ADULT; CARBON DIOXIDE; CARBON RADIOISOTOPES; CELL LINE, TRANSFORMED; CHILD; CHILD, PRESCHOOL; GALACTOSE; GALACTOSEMIAS; GLUCOSE; HERPESVIRUS 4, HUMAN; HOMOZYGOTE; HUMANS; KINETICS; LYMPHOCYTES; MUTATION; OXIDATION-REDUCTION; UTP-HEXOSE-1-PHOSPHATE URIDYLYLTRANSFERASE;

EID: 0034834630     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1010529629750     Document Type: Article

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