Mitochondrial import and processing of wild type and Type III mutant isovaleryl-CoA dehydrogenase

Journal of Biological Chemistry

Volumn 275, Issue 11, 2000, Pages 7958-7963

  Volchenboum, Samuel L ^b,c   Vockley, Jerry ^a,b  

^a MAYO CLINIC   (United States)

^b MAYO GRADUATE SCHOOL   (United States)

^c CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ISOVALERIC ACID; ISOVALERYL COENZYME A DEHYDROGENASE; UNCLASSIFIED DRUG;

ACIDEMIA; ARTICLE; CARBOXY TERMINAL SEQUENCE; CRYSTAL STRUCTURE; ENZYME ACTIVITY; FIBROBLAST; GENE DELETION; HUMAN; IN VITRO STUDY; MITOCHONDRIAL RESPIRATION; PRIORITY JOURNAL; SEQUENCE ANALYSIS;

ACYL COENZYME A; AMINO ACID METABOLISM, INBORN ERRORS; AMINO ACID SEQUENCE; BIOLOGICAL TRANSPORT; ENZYME STABILITY; HUMANS; ISOVALERYL-COA DEHYDROGENASE; LEUCINE; MITOCHONDRIA; MODELS, MOLECULAR; MOLECULAR SEQUENCE DATA; MUTATION; OPEN READING FRAMES; OXIDOREDUCTASES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; PENTANOIC ACIDS; PROTEIN CONFORMATION; PROTEIN PROCESSING, POST-TRANSLATIONAL; SEQUENCE HOMOLOGY, AMINO ACID;

ESCHERICHIA COLI;

EID: 0034677759     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.275.11.7958     Document Type: Article

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