Application of the obligate aerobic yeast Yarrowia lipolytica as a eucaryotic model to analyse Leigh syndrome mutations in the complex I core subunits PSST and TYKY

Biochimica et Biophysica Acta - Bioenergetics

Volumn 1459, Issue 2-3, 2000, Pages 258-265

  Ahlers, Pamela M ^a   Garofano, Aurelio ^a   Kerscher, Stefan J ^a   Brandt, Ulrich ^a  

^a UNIVERSITY HOSPITAL FRANKFURT   (Germany)

Author keywords

Complex I; Leigh syndrome; Mitochondria; Point mutation; Yarrowia lipolytica; Yeast

Indexed keywords

REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); UBIQUINONE;

ARTICLE; CONTROLLED STUDY; LEIGH DISEASE; MITOCHONDRIAL MEMBRANE; MUTATION; NONHUMAN; POINT MUTATION; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; SITE DIRECTED MUTAGENESIS; STRUCTURE ACTIVITY RELATION; YARROWIA LIPOLYTICA; YEAST;

AMINO ACID SEQUENCE; ASCOMYCOTA; ELECTRON TRANSPORT COMPLEX I; HUMANS; KINETICS; LEIGH DISEASE; MOLECULAR SEQUENCE DATA; MUTAGENESIS, SITE-DIRECTED; MUTATION; NADH, NADPH OXIDOREDUCTASES; SEQUENCE ALIGNMENT;

BOVINAE; EUKARYOTA; GENETTA; YARROWIA LIPOLYTICA;

EID: 0034663704     PISSN: 00052728     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0005-2728(00)00160-2     Document Type: Article

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