Enantioselective analysis of ketone bodies in patients with β-ketothiolase deficiency, medium-chain acyl coenzyme A dehydrogenase deficiency and ketonemic vomiting

Journal of Chromatography B: Biomedical Sciences and Applications

Volumn 739, Issue 2, 2000, Pages 313-324

  Heil, Martin ^a   Podebrad, Frank ^a   Prado, Elisa ^a   Beck, Thomas ^a   Mosandl, Armin ^a   Sewell, Adrian C ^b   Böhles, Hans ^b   Lehnert, Willy ^c  

^a GOETHE UNIVERSITY   (Germany)

^b UNIVERSITY HOSPITAL FRANKFURT   (Germany)

^c UNIVERSITY OF FREIBURG   (Germany)

Author keywords

Ketothiolase; 3 Hydroxy 2 methylbutanoic acid; 3 Hydroxybutanoic acid; Enantiomer separation; Ketone bodies

Indexed keywords

3 HYDROXY 2 METHYLBUTYRIC ACID; 3 HYDROXYBUTYRIC ACID; ACETYL COENZYME A ACYLTRANSFERASE; ACYL COENZYME A DEHYDROGENASE; KETONE BODY; UNCLASSIFIED DRUG;

AMINO ACID ANALYSIS; AMINO ACID METABOLISM; ARTICLE; CLINICAL ARTICLE; ENANTIOMER; ENZYME DEFICIENCY; ESTERIFICATION; GAS CHROMATOGRAPHY; HUMAN; KETOGENESIS; MASS SPECTROMETRY; PRIORITY JOURNAL; VOMITING;

ACETYL-COA C-ACYLTRANSFERASE; ACYL-COA DEHYDROGENASE; CHILD; FATTY ACID DESATURASES; GAS CHROMATOGRAPHY-MASS SPECTROMETRY; HUMANS; KETONE BODIES; MALE; METABOLISM, INBORN ERRORS; OXIDATION-REDUCTION; VOMITING;

EID: 0034628992     PISSN: 13872273     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0378-4347(00)00022-0     Document Type: Article

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