-
1
-
-
0023039337
-
Behavioral and neurotransmitter changes in the urease-infused rat, a model of congenital hyperammonemia
-
Batshaw M.L., Hyman S.L., Mellits E.D., Thomas G.H., DeMuro R., Coyle J.T. Behavioral and neurotransmitter changes in the urease-infused rat, a model of congenital hyperammonemia. Pediatr. Res. 20:1986;1310-1315.
-
(1986)
Pediatr. Res.
, vol.20
, pp. 1310-1315
-
-
Batshaw, M.L.1
Hyman, S.L.2
Mellits, E.D.3
Thomas, G.H.4
Demuro, R.5
Coyle, J.T.6
-
2
-
-
0041960733
-
Animal models of congenital hyperammonemia
-
J.T. Coyle. New York: Liss
-
Batshaw M.L., Hyman S.L., Bachmann C., Qureshi I.A., Coyle J.T. Animal models of congenital hyperammonemia. Coyle J.T. Animal Models of Dementia. 1987;163-198 Liss, New York.
-
(1987)
Animal Models of Dementia
, pp. 163-198
-
-
Batshaw, M.L.1
Hyman, S.L.2
Bachmann, C.3
Qureshi, I.A.4
Coyle, J.T.5
-
3
-
-
0029561659
-
The sparse fur mouse as a model for gene therapy in ornithine carbamoyltransferase deficiency
-
Batshaw M.L., Yudkoff M., McLaughlin B.A., Gorry E., Anegawa N.J., Smith I.A.S., Hyman S.L., Robinson M.B. The sparse fur mouse as a model for gene therapy in ornithine carbamoyltransferase deficiency. Gene Ther. 2:1995;743-749.
-
(1995)
Gene Ther.
, vol.2
, pp. 743-749
-
-
Batshaw, M.L.1
Yudkoff, M.2
McLaughlin, B.A.3
Gorry, E.4
Anegawa, N.J.5
Smith, I.A.S.6
Hyman, S.L.7
Robinson, M.B.8
-
4
-
-
0031762572
-
Evidence for a central cholinergic deficit in congenital ornithine transcarbamylase deficiency
-
Butterworth R.F. Evidence for a central cholinergic deficit in congenital ornithine transcarbamylase deficiency. Dev. Neurosci. 20:1998;478-484.
-
(1998)
Dev. Neurosci.
, vol.20
, pp. 478-484
-
-
Butterworth, R.F.1
-
5
-
-
0042461295
-
Abnormal ornithine carbamoyltransferase in mice having the sparse-fur mutation
-
DeMars R., LeVan S.L., Trend B.L., Russell L.B. Abnormal ornithine carbamoyltransferase in mice having the sparse-fur mutation. Proc. Natl. Acad. Sci. USA. 73:1976;1693-1697.
-
(1976)
Proc. Natl. Acad. Sci. USA
, vol.73
, pp. 1693-1697
-
-
Demars, R.1
Levan, S.L.2
Trend, B.L.3
Russell, L.B.4
-
6
-
-
0000147466
-
An ion exchange method for plasma ammonia concentration
-
Dienst S.G. An ion exchange method for plasma ammonia concentration. J. Lab. Clin. Med. 58:1961;149-155.
-
(1961)
J. Lab. Clin. Med.
, vol.58
, pp. 149-155
-
-
Dienst, S.G.1
-
7
-
-
0023269882
-
Ammonia-induced release of neurotransmitters from rat brain synaptosomes: Differences between the effects on amines and amino acids
-
Erecinska A., Pastuszko A., Wilson D.F., Nelson D. Ammonia-induced release of neurotransmitters from rat brain synaptosomes: differences between the effects on amines and amino acids. J. Neurochem. 49:1987;1258-1265.
-
(1987)
J. Neurochem.
, vol.49
, pp. 1258-1265
-
-
Erecinska, A.1
Pastuszko, A.2
Wilson, D.F.3
Nelson, D.4
-
8
-
-
0016372827
-
Brain histology and behavior of mice injected with urease
-
Gibson G.E., Zimber A., Krook L., Richardson E.P., Visek W.J. Brain histology and behavior of mice injected with urease. J. Neuropathol. Exp. Neurol. 33:1974;201-211.
-
(1974)
J. Neuropathol. Exp. Neurol.
, vol.33
, pp. 201-211
-
-
Gibson, G.E.1
Zimber, A.2
Krook, L.3
Richardson, E.P.4
Visek, W.J.5
-
11
-
-
0023478104
-
Accumulation of large neutral amino acids in the brain of sparse-fur mice at hyperammonemic state
-
Inoue I., Gushiken T., Kobayashi K., Saheki T. Accumulation of large neutral amino acids in the brain of sparse-fur mice at hyperammonemic state. Biochem. Med. Metab. Biol. 38:1987;378-386.
-
(1987)
Biochem. Med. Metab. Biol.
, vol.38
, pp. 378-386
-
-
Inoue, I.1
Gushiken, T.2
Kobayashi, K.3
Saheki, T.4
-
12
-
-
0033506343
-
Neonatal onset ornithine transcarbamylase deficiency: A retrospective analysis
-
Maestri N.E., Clissold D., Brusilow S.W. Neonatal onset ornithine transcarbamylase deficiency: a retrospective analysis. J. Pediatr. 134:1999;268-272.
-
(1999)
J. Pediatr.
, vol.134
, pp. 268-272
-
-
Maestri, N.E.1
Clissold, D.2
Brusilow, S.W.3
-
13
-
-
0032472416
-
Impaired learning in rats in a 14-unit T-maze by 7-nitroindazole, a neuronal nitric oxide synthase inhibitor, is attenuated by the nitric oxide donor, molsidomine
-
Meyer R.C., Spangler E.L., Patel N., London E.D., Ingram D.K. Impaired learning in rats in a 14-unit T-maze by 7-nitroindazole, a neuronal nitric oxide synthase inhibitor, is attenuated by the nitric oxide donor, molsidomine. Eur. J. Pharmacol. 341:1998;17-22.
-
(1998)
Eur. J. Pharmacol.
, vol.341
, pp. 17-22
-
-
Meyer, R.C.1
Spangler, E.L.2
Patel, N.3
London, E.D.4
Ingram, D.K.5
-
14
-
-
0021187612
-
Neurologic outcome in children with inborn errors of urea synthesis
-
Msall M., Batshaw M.L., Suss R., Brusilow S.W., Mellits E.D. Neurologic outcome in children with inborn errors of urea synthesis. N. Engl. J. Med. 310:1984;1500-1505.
-
(1984)
N. Engl. J. Med.
, vol.310
, pp. 1500-1505
-
-
Msall, M.1
Batshaw, M.L.2
Suss, R.3
Brusilow, S.W.4
Mellits, E.D.5
-
15
-
-
0025886368
-
Retrospective study of urea cycle disorders. Part 2: Neurological outcome in forty-nine Japanese patients with urea cycle enzymopathies
-
Nagata N., Matsuda I., Matsuura T., Oyanagi K., Tada K., Narisawa K., Kitagawa T., Sakiyama T., Yamashita F., Yoshino M. Retrospective study of urea cycle disorders. Part 2: Neurological outcome in forty-nine Japanese patients with urea cycle enzymopathies. Am. J. Med. Genet. 40:1991;477-481.
-
(1991)
Am. J. Med. Genet.
, vol.40
, pp. 477-481
-
-
Nagata, N.1
Matsuda, I.2
Matsuura, T.3
Oyanagi, K.4
Tada, K.5
Narisawa, K.6
Kitagawa, T.7
Sakiyama, T.8
Yamashita, F.9
Yoshino, M.10
-
16
-
-
0018384552
-
Ornithine transcarbamylase deficiency in mutant mice. I. Studies on the characterization of enzyme defect and suitability as animal model of human disease
-
Qureshi I.A., Letarte J., Ouellet R. Ornithine transcarbamylase deficiency in mutant mice. I. Studies on the characterization of enzyme defect and suitability as animal model of human disease. Pediatr. Res. 13:1979;807-811.
-
(1979)
Pediatr. Res.
, vol.13
, pp. 807-811
-
-
Qureshi, I.A.1
Letarte, J.2
Ouellet, R.3
-
17
-
-
0042962459
-
Spontaneous animal models of ornithine transcarbamylase deficiency, studies on serum and nitrogen metabolites
-
A. Lowenthal, A. Mori, & B. Marescau. New York: Plenum Press
-
Qureshi I.A., Letarte J., Ouellet R. Spontaneous animal models of ornithine transcarbamylase deficiency, studies on serum and nitrogen metabolites. Lowenthal A., Mori A., Marescau B. Urea Cycle Diseases. 1983;173-183 Plenum Press, New York.
-
(1983)
Urea Cycle Diseases
, pp. 173-183
-
-
Qureshi, I.A.1
Letarte, J.2
Ouellet, R.3
-
18
-
-
0030846740
-
Sparse-fur (spf) mouse as a model of hyperammonemia, alterations in the neurotransmitter systems
-
Qureshi I.A., Rama Rao K.V. Sparse-fur (spf) mouse as a model of hyperammonemia, alterations in the neurotransmitter systems. Adv. Exp. Med. Biol. 420:1997;143-158.
-
(1997)
Adv. Exp. Med. Biol.
, vol.420
, pp. 143-158
-
-
Qureshi, I.A.1
Rama Rao, K.V.2
-
19
-
-
0030582438
-
Arginine-related guanidino compounds and nitric oxide synthase in the brain of ornithine trnascarbamylase deficient spf mutant mouse: Effect of metabolic arginine deficiency
-
Ratnakumari L., Qureshi I.A., Butterworth R.F., Marescau B., De Deyn P.P. Arginine-related guanidino compounds and nitric oxide synthase in the brain of ornithine trnascarbamylase deficient spf mutant mouse: effect of metabolic arginine deficiency. Neurosci. Lett. 215:1996;153-156.
-
(1996)
Neurosci. Lett.
, vol.215
, pp. 153-156
-
-
Ratnakumari, L.1
Qureshi, I.A.2
Butterworth, R.F.3
Marescau, B.4
De Deyn, P.P.5
-
20
-
-
0017155049
-
X-Chromosome inactivation in human liver, confirmation of X-linkage of ornithine transcarbamylase
-
Ricciuti F., Gelehrter T.D., Rosenberg L.E. X-Chromosome inactivation in human liver, confirmation of X-linkage of ornithine transcarbamylase. Am. J. Hum. Genet. 28:1976;332-338.
-
(1976)
Am. J. Hum. Genet.
, vol.28
, pp. 332-338
-
-
Ricciuti, F.1
Gelehrter, T.D.2
Rosenberg, L.E.3
-
21
-
-
0031405611
-
The role of nitric oxide in passive avoidance learning
-
Telegdy G., Kokavszky R. The role of nitric oxide in passive avoidance learning. Neuropharmacology. 36:1997;1583-1587.
-
(1997)
Neuropharmacology
, vol.36
, pp. 1583-1587
-
-
Telegdy, G.1
Kokavszky, R.2
-
22
-
-
0033506342
-
Treatment of urea cycle disorders
-
Thoene J.G. Treatment of urea cycle disorders. J. Pediatr. 134:1999;255-256.
-
(1999)
J. Pediatr.
, vol.134
, pp. 255-256
-
-
Thoene, J.G.1
-
23
-
-
0023663546
-
The molecular basis of the sparse fur mouse mutation
-
Veres G., Gibbs R.A., Scherer S.E., Caskey C.T. The molecular basis of the sparse fur mouse mutation. Science. 237:1987;415-417.
-
(1987)
Science
, vol.237
, pp. 415-417
-
-
Veres, G.1
Gibbs, R.A.2
Scherer, S.E.3
Caskey, C.T.4
-
24
-
-
0032029111
-
Nitric oxide synthase inhibitors impair reference memory formation in a radial arm maze task in rats
-
Zou L.B., Yamada K., Tanaka T., Kameyama T., Nabeshima T. Nitric oxide synthase inhibitors impair reference memory formation in a radial arm maze task in rats. Neuropharmacology. 37:1998;323-330.
-
(1998)
Neuropharmacology
, vol.37
, pp. 323-330
-
-
Zou, L.B.1
Yamada, K.2
Tanaka, T.3
Kameyama, T.4
Nabeshima, T.5
|