New insights into the assembly of extracellular microfibrils from the analysis of the fibrillin 1 mutation in the Tight skin mouse

Journal of Cell Biology

Volumn 150, Issue 3, 2000, Pages 667-679

  Gayraud, B ^a   Keene, D R ^a   Sakai, L Y ^a   Ramirez, F ^a  

^a NEW YORK UNIVERSITY   (United States)

Author keywords

Elastic fibers; Extracellular matrix; Marfan syndrome; Microfibrils; Tsk

Indexed keywords

FIBRILLIN;

ANIMAL CELL; ARTICLE; CONTROLLED STUDY; ELASTIC FIBER; EXTRACELLULAR MATRIX; FIBER; GENE MUTATION; MARFAN SYNDROME; MOUSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DEGRADATION; PROTEIN POLYMERIZATION; VASCULAR DISEASE;

ALLELES; ANIMALS; CARDIOVASCULAR ABNORMALITIES; CROSSES, GENETIC; EXTRACELLULAR MATRIX; EXTRACELLULAR MATRIX PROTEINS; GENE DUPLICATION; GENES, DOMINANT; GENES, LETHAL; GENOTYPE; HETEROZYGOTE; HOMOZYGOTE; MARFAN SYNDROME; MICE; MICE, MUTANT STRAINS; MICROFILAMENT PROTEINS; PHENOTYPE; PROTEIN CONFORMATION; SKIN ABNORMALITIES;

ANIMALIA; RODENTIA;

EID: 0034617999     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.150.3.667     Document Type: Article

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