Familial British dementia: Expression and metabolism of BRI

Annals of the New York Academy of Sciences

Volumn 920, Issue , 2000, Pages 93-99

  Seong Hun, K I M ^a   Wang, Rong ^b   Gordon, David J ^a   Bass, Joseph ^a   Steiner, Donald F ^a   Thinakaran, Gopal ^a   Lynn, David G ^b   Meredith, Stephen C ^a   Sisodia, Sangram S ^a  

^a UNIVERSITY OF CHICAGO   (United States)

^b ROCKEFELLER UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMYLOID; ARGININE; FURIN; MEMBRANE PROTEIN; PROTEIN BRI; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; CARBOXY TERMINAL SEQUENCE; CODON; CONFERENCE PAPER; CONFORMATION; DEGENERATIVE DISEASE; ELECTRON MICROSCOPY; FAMILIAL BRITISH DEMENTIA; GENETIC DISORDER; HUMAN; PATHOGENESIS; PROTEIN EXPRESSION; PROTEIN FAMILY; PROTEIN METABOLISM; PROTEIN PROCESSING; RNA TRANSLATION; SEQUENCE ANALYSIS;

EID: 0034531673     PISSN: 00778923     EISSN: None     Source Type: Book Series    
DOI: 10.1111/j.1749-6632.2000.tb06909.x     Document Type: Conference Paper

References (17)

1. Familial cerebral amyloid angiopathy with nonneuritic amyloid plaque formation
2. A form of familial presenile dementia with spastic paralysis (including the pathological examination of a case)
3. Congophilic angiopathy of the brain: A clinical and pathological report on two siblings
4. A stop-codon mutation in the BRI gene associated with familial British dementia
5. Furin: A mammalian subtilisin/Kex2p-like endoprotease involved in processing of a wide variety of precursor proteins
6. Bi-cycling the furin pathway: From TGN localization to pathogen activation and embryogenesis
7. Furin mediates enhanced production of fibrillogenic ABri peptides in familial British dementia
8. Sequence requirements for precursor cleavage within the constitutive secretory pathway
9. Positional and additive effects of basic amino acids on processing of precursor proteins within the constitutive secretory pathway
10. Human furin is a calcium-dependent serine endoprotease that recognizes the sequence Arg-X-X-Arg and efficiently cleaves anthrax toxin protective antigen
11. Sequence requirements for endoproteolytic processing of precursor proteins by furin: Transfection and in vitro experiments
12. Strains of CHO-K1 cells resistant to Pseudomonas exotoxin A and cross-resistant to diphtheria toxin and viruses
13. Expression of mouse furin in a Chinese hamster cell resistant to Pseudomonas exotoxin A and viruses complements the genetic lesion
14. Analysis of mutations in alleles of the fur gene from an endoprotease-deficient Chinese hamster ovary cell strain
15. Isolation of markers for chondro-osteogenic differentiation using cDNA library subtraction. Molecular cloning and characterization of a gene belonging to a novel multigene family of integral membrane proteins
16. cDNA sequence analysis, chromosomal assignment and expression pattern of the gene coding for integral membrane protein 2B
17. Regulation of bone morphogenetic protein activity by pro domains and proprotein convertases