Defect in N-glycosylation of proteins is tissue-dependent in Congenital Disorders of Glycosylation Ia

Glycobiology

Volumn 10, Issue 12, 2000, Pages 1277-1281

  Dupré, Thierry ^a   Barnier, Anne ^a   De Lonlay, Pascale ^b   Cormier Daire, Valérie ^b   Durand, Geneviève ^a,d   Codogno, Patrice ^c   Seta, Nathalie ^a,e  

^a BICHAT HOSPITAL   (France)

^b HÔPITAL NECKER ENFANTS MALADES   (France)

^c INSERM   (France)

^d UNIVERSITÉ PARIS SACLAY   (France)

^e UNIVERSITÉ PARIS DESCARTES   (France)

Author keywords

CDG; GLUT 1; Immunoglobulin G; Protein glycosylation; 1 antitrypsin

Indexed keywords

ALPHA 1 ANTITRYPSIN; GLUCOSE TRANSPORTER; GLYCOPROTEIN; IMMUNOGLOBULIN G; MEMBRANE PROTEIN;

ARTICLE; BIOCHEMISTRY; CONGENITAL DISORDER OF GLYCOSYLATION; CONTROLLED STUDY; FIBROBLAST; GENE EXPRESSION; GLUCOSE TRANSPORT; HUMAN; HUMAN CELL; INTESTINE CELL; KERATINOCYTE; LEUKOCYTE; PHENOTYPE; PRIORITY JOURNAL; PROTEIN GLYCOSYLATION; PROTEIN ISOLATION; SERUM; WESTERN BLOTTING;

EID: 0034491915     PISSN: 09596658     EISSN: None     Source Type: Journal    
DOI: 10.1093/glycob/10.12.1277     Document Type: Article

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