Loss of oxidation-reduction specificity in amyotrophic lateral sclerosis-associated CuZnSOD mutants

Journal of Molecular Neuroscience

Volumn 15, Issue 2, 2000, Pages 71-83

  Cafe, C ^a   Testa, M P ^a   Sheldon, P J ^a   French, W P ^a   Ellerby, L M ^b   Bredesen, D E ^b  

^a BURNHAM INSTITUTE   (United States)

^b BUCK INSTITUTE FOR RESEARCH ON AGING   (United States)

Author keywords

Neurodegeneration; Peroxides; Reactive oxygen species; Spectrum; Superoxide dismutase

Indexed keywords

ASCORBIC ACID; COPPER; COPPER ZINC SUPEROXIDE DISMUTASE; MUTANT PROTEIN; PEROXIDASE; PEROXIDE; REACTIVE OXYGEN METABOLITE;

AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVE SITE; ENZYME ACTIVITY; ENZYME DEGRADATION; ENZYME INACTIVATION; GENE MUTATION; MOTONEURON; NERVE CELL DEGENERATION; NEUROTOXICITY; NONHUMAN; OXIDATION REDUCTION REACTION; OXIDATIVE STRESS; SPECTRUM;

AMINO ACID SUBSTITUTION; HUMANS; KINETICS; MOTOR NEURON DISEASE; MUTATION; OXIDATION-REDUCTION; RECOMBINANT PROTEINS; SPECTROPHOTOMETRY; SUPEROXIDE DISMUTASE;

EID: 0034490005     PISSN: 08958696     EISSN: None     Source Type: Journal    
DOI: 10.1385/JMN:15:2:71     Document Type: Article

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