Clinical and EEG video-polygraphic features of epileptic spasms in a child with dihydropteridine reductase deficiency. Efficiency of hydrocortisone

Epileptic Disorders

Volumn 2, Issue 4, 2000, Pages 213-217

  Mikaeloff, Y ^a   Plouin, P ^a   Dhondt, J L ^a   Ponsot, G ^a   Dulac, O ^a  

^a HÔPITAL SAINT VINCENT DE PAUL   (France)

Author keywords

Biopterin deficiency; Dihydropteridin reductase deficiency; EEG video polygraphy; Epileptic spasms; Steroid treatment

Indexed keywords

CLONAZEPAM; DIHYDROPTERIDINE REDUCTASE; HYDROCORTISONE;

ARTICLE; CASE REPORT; CHILD; CLINICAL FEATURE; CORTICOSTEROID THERAPY; DIET RESTRICTION; DRUG EFFICACY; ELECTROENCEPHALOGRAM; ENZYME DEFICIENCY; EPILEPSY; HUMAN; INFANTILE SPASM; MALE; MULTICHANNEL RECORDER; PRESCHOOL CHILD; PRIORITY JOURNAL; TREATMENT OUTCOME; VIDEORECORDING; WEST SYNDROME;

ANTI-INFLAMMATORY AGENTS; ANTICONVULSANTS; CHILD; ELECTROENCEPHALOGRAPHY; EPILEPSIES, MYOCLONIC; HUMANS; HYDROCORTISONE; INFANT, NEWBORN; MALE; PHENYLKETONURIAS; SEVERITY OF ILLNESS INDEX; SPASMS, INFANTILE; TREATMENT OUTCOME; VIDEO RECORDING;

EID: 0034486871     PISSN: 12949361     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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