Congenital hepatic fibrosis with fatal cholestatic liver damage

Internal Medicine

Volumn 39, Issue 11, 2000, Pages 930-935

  Takatori, Masao ^a   Iwabuchi, Shogo ^a   Hayashi, Takeshi ^a   Takahashi, Yasuto ^a   Suzuki, Michihiro ^a   Iino, Shiro ^a   Maeyama, Shiro ^a   Uchikoshi, Toshiyuki ^a  

^a ST MARIANNA UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Hepatic failure; Hepatic fibrosis; Portal hypertension; Transplantation

Indexed keywords

ADOLESCENT; ARTICLE; CASE REPORT; FATALITY; HUMAN; INTRAHEPATIC CHOLESTASIS; LIVER CIRRHOSIS; MALE; PATHOLOGY;

ADOLESCENT; CHOLESTASIS, INTRAHEPATIC; FATAL OUTCOME; HUMANS; LIVER CIRRHOSIS; MALE;

EID: 0034328240     PISSN: 09182918     EISSN: None     Source Type: Journal    
DOI: 10.2169/internalmedicine.39.930     Document Type: Article

References (24)

1. Popper H, Ramalingaswami V, Miyaji T, Baggenstoss AH. Cirrosis in: Diseases of the liver and biliary tract. Standardization and nomenclature, diagnostic criteria and diagnostic methodology. Fogarty international center proceedings no. 22 Leevey CM, Popper H, Sherlock S, Eds. DHEW Publication No. (NIH) 76-725, 23-24, 1976.
2. Schwartz SI, Dale WA. Primary sclerosing cholangitis. Arch Surg 77: 439-451, 1958.
3. Manesis JG, Sullivan JF. Primary sclerosing cholangitis. Arch Intern Med 115: 137-139, 1965.
4. Bhathal PS, Powell LN. Primary intrahepatic obliterating cholangitis: a possible variant of 'sclerosing cholangitis'. Gut 10: 887-893, 1969.
5. Wiesner RH, LaRusso NF, Ludwig J, Dickson RE. Comparison of the clinicopathologic features of primary sclerosing cholangitis and primary biliary cirrhosis. Gastroenterology 88: 108-114, 1985.
6. Harrison RF, Hubscher SG. The spectrum of bile duct lesions in end-stage primary sclerosing cholangitis. Histopathology 19: 321-327, 1991.
7. Clayton RJ, Iber FL, Ruebner BH, McKusick VA. Byler disease. Am J Dis Child 117: 112-124, 1969.
8. Alagille D. Intra-hepatic billiary atresia (hepatic ductular hypoplasia). in: Liver Diseases in Infancy and Childhood, Berenberg SR, Ed. Netherlands: Martinus Nijhoff Medical Division, 1976: 129-142.
9. Watson GH, Miller V. Arteriohepatic dysplasia-familial pulmonary arterial stenosis with neonatal liver disease. Arch Dis Child 48: 459-466, 1973.
10. Aagenaes O, Van Der Hagen CB, Refsum S. Hereditary recurrent intrahepatic cholestasis from birth. Arch Dis Child 43: 646-657, 1968.
11. Nezelof C, Dupart MC, Jaubert F, Eliacher E. A lethal familial syndrome associating arthrogryposis multiplex congenita, renal dysfunction, and a cholestatic and pigmentary liver disease. J Pediatr 94:258-260,1979.
12. Kerr DNS, Harrison CV, Sherlock S, Walker RM. Congenital hepatic fibrosis. Quart J M 30: 91-117, 1961.
13. Alvarez F, Bernard O, Brunelle F, et al. Congenital hepatic fibrosis in children. J Pediatr 99: 370-375, 1981.
14. Ghishan FK, Younoszai MK. Congenital hepatic fibrosis: a disease with diverse manifestations. Am J Gastroenterol 75: 317-320, 1981.
15. Sommerschild HC, Langmark F, Maurseth K. Congenital hepatic fibrosis: report of two new cases and review of the literature. Surgery 73: 53-58, 1973.
16. Perisic VN. Long-term studies on congenital hepatic fibrosis in children. Acta Paediatr 84: 695-696, 1995.
17. Ishak KG. Nodular regenerative hyperplasia, blood disorders and other uncommon diseases; Associated with intrahepatic portal hypertension, in: Portal Hypertension. Clinical and physical aspects, Okuda K, Benhamou J-P Eds., Springer-Verlag, Tokyo, 1991: 325-342.
18. Stromeyer FW, Ishak KG. Nodular transformation (nodular "regenera-tive" hyperplasia) of the liver. A cilinicopathologic study of 30 cases. Hum Pathol 12: 60-71, 1981.
19. Steiner PE. Nodular regenerative hyperplasia of the liver. Am J Pathol 35: 943-953, 1959.
20. Blendis LM, Parkinson MC, Shilkin KB, Williams R. Nodular regenerative hyperplasia of the liver in Felly's syndrome. Q J Med 43: 25-32, 1974.
21. Wanless IR, Godwin TA, Allen F, Feder A. Nodular regenerative hyperplasia of the liver in hematologic disorders: A possible response to obliterative portal venopathy. A morphometric study of nine cases with an hypothesis on the pathogenesis. Medicine (Baltimore) 59: 367-379, 1980.
22. Thung SN, Gerber MA, Bodenheimer HC Jr. Nodular regenerative hyperplasia of the liver in a patient with diabetes mellitus. Cancer 49: 543-546, 1982.
23. Rougier P, Degott C, Rueff B, Benhamou J-P. Nodular regenerative hyperplasia of the liver. Report of six cases and review of the literature. Gastroenterology 75: 169-172, 1978.
24. Kuramochi S, Tashiro M, Torigata C, et al. The three patients of SLE complicated with multiple nodular hyperplasia. Proc Jpn Soc Pathol 67: 317-318, 1978 (Abstract in Japanese).