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Microscopy Research and Technique

Volumn 50, Issue 1, 2000, Pages 10-15

Neuropathology of Gerstmann-Straussler-Scheinker disease

(6) Bugiani, Orso a Giaccone, Giorgio a Piccardo, Pedro b Morbin, Michela a Tagliavini, Fabrizio a Ghetti, Bernardino b

a DEPARTMENT OF NEUROSURGERY (Italy)

b INDIANA UNIVERSITY (United States)

Author keywords

Amyloidosis; Gerstmann Straussler Syndrome; Prion diseases

Indexed keywords

DEPOSITS; GENES; GLYCOPROTEINS; NEURONS; PHOSPHORUS COMPOUNDS; PRASEODYMIUM COMPOUNDS; PROTEINS; NEURODEGENERATIVE DISEASES;

AMYLOID DEPOSITS; AMYLOIDOSIS; BASAL GANGLIA; CEREBELLAR CORTEX; CEREBRAL CORTEX; COGNITIVE DECLINE; GERSTMANN-STRAUSSL SYNDROME; LOCALISED; NEURODEGENERATION; PRION DISEASE; GERSTMANN-STRÄUSSLE SYNDROME;

NEURODEGENERATIVE DISEASES; PROTEINS;

AMYLOID PROTEIN; PRION PROTEIN; AMYLOID; INFECTIOUS AMYLOID PRECURSOR PROTEIN; PRNP PROTEIN, HUMAN; PROTEIN PRECURSOR;

AMYLOIDOSIS; ARTICLE; BASAL GANGLION; BRAIN CORTEX; CLINICAL FEATURE; DNA POLYMORPHISM; GENE MUTATION; GERSTMANN STRAUSSLER SCHEINKER SYNDROME; HUMAN; HUMAN TISSUE; IMMUNOREACTIVITY; NEUROPATHOLOGY; PRIORITY JOURNAL; ANIMAL; BRAIN; CEREBELLUM CORTEX; CHEMISTRY; ELECTRON MICROSCOPY; GENETIC POLYMORPHISM; GENETICS; GLIOSIS; IMMUNOHISTOCHEMISTRY; LEWY BODY; MUTATION; NEURITE; NEUROFIBRILLARY TANGLE; PATHOLOGY; PRION; REVIEW; SENILE PLAQUE; ULTRASTRUCTURE;

AMYLOID; ANIMALS; BASAL GANGLIA; BRAIN; CEREBELLAR CORTEX; CEREBRAL CORTEX; GERSTMANN-STRAUSSLER-SCHEINKER DISEASE; GLIOSIS; HUMANS; IMMUNOHISTOCHEMISTRY; LEWY BODIES; MICROSCOPY, ELECTRON; MUTATION; NEURITES; NEUROFIBRILLARY TANGLES; POLYMORPHISM, GENETIC; PRIONS; PROTEIN PRECURSORS; SENILE PLAQUES;

EID: 0034214842 PISSN: 1059910X EISSN: None Source Type: Journal
DOI: 10.1002/1097-0029(20000701)50:1<10::AID-JEMT3>3.0.CO;2-6 Document Type: Article

Times cited : (50)

References (26)

1
- 0028143841
- Mouse cortical cells lacking cellular PrP survive in culture with a neurotexic PrP fragment
- (1996) Neuroreport , vol.5 , pp. 2057-2060
- Brown, D.R.¹ Herms, J.² Kretzschmar, H.A.³

2
- 0027531316
- βPP participates in PrP-amyloid plaques in Gerstmann-Straussler-Scheinker disease, Indiana kindred
- (1993) J Neuropathol Exp Neurol , vol.52 , pp. 64-70
- Bugiani, O.¹ Giaccone, G.² Verga, L.³ Pollo, B.⁴ Frangione, B.⁵ Farlow, M.R.⁶ Tagliavini, F.⁷ Ghetti, B.⁸

3
- 0001046761
- Apolipoprotein E and J immunoreactivity in Gerstmann-Straussler-Scheinker disease
- (1994) Neurobiol Aging , vol.15
- Bugiani, O.¹ Giaccone, G.² Frigerio, L.³ Farlow, M.R.⁴ Ghetti, B.⁵ Tagliavini, F.⁶

4
- 0008545743
- Gerstmann-Straussler-Scheinker disease
- Vinken PJ, et al., editors. Handbook of clinical neurology, Amsterdam: Elsevier Science BV
- (1991) , vol.16 , pp. 619-633
- Farlow, M.R.¹ Tagliavini, F.² Bugiani, O.³ Ghetti, B.⁴

5
- 0027483615
- Neurotoxicity of a prion protein fragment
- (1993) Nature , vol.362 , pp. 543-546
- Forloni, G.¹ Angeretti, N.² Chiesa, R.³ Monzani, E.⁴ Salmona, M.⁵ Bugiani, O.⁶ Tagliavini, F.⁷

6
- 0001385519
- Uber ein noch nicht beschriebenes Reflexphagnomen bei einer Erkrankung des zerebellaren Systems
- (1928) Wien Med Wochenschr , vol.78 , pp. 906-908
- Gerstmann, J.¹

7
- 51849178459
- Uber eine eigenartige hereditar-familiare Erkrankung des Zentralnervensystems. Zugleich ein Beitrag zur Frage des vorzeitigen lokalen Alters
- (1936) Z Neur Psychiat , vol.154 , pp. 736-762
- Gerstmann, J.¹ Straussler, E.² Scheinker, I.³

8
- 0024856333
- Gerstmann-Straussler-Scheinker disease. II. Neurofibrillary tangles and plaques with PrP-amyloid coexist in an affected family
- (1989) Neurology , vol.38 , pp. 1453-1461
- Ghetti, B.¹ Tagliavini, F.² Masters, C.L.³ Beyreuther, K.⁴ Giaccone, G.⁵ Verga, L.⁶ Farlow, M.R.⁷ Conneally, P.M.⁸ Dlouhy, S.R.⁹ Azzarelli, B.¹⁰ Bugiani, O.¹¹

9
- 0028984802
- Gerstmann-Straussler-Scheinker disease and the Indiana kindred
- (1995) Brain Pathol , vol.5 , pp. 61-75
- Ghetti, B.¹ Dlouhy, S.R.² Giaccone, G.³ Bugiani, O.⁴ Frangione, B.⁵ Farlow, M.R.⁶ Tagliavini, F.⁷

10
- 15844415943
- Prion protein amyloidosis
- (1996) Brain Pathol , vol.6 , pp. 127-145
- Ghetti, B.¹ Piccardo, P.² Frangione, B.³ Bugiani, O.⁴ Giaccone, G.⁵ Young, K.⁶ Prelli, F.⁷ Farlow, M.R.⁸ Dlouhy, S.R.⁹ Tagliavini, F.¹⁰

11
- 0025013882
- Neurofibrillary tangles of the Indiana kindred of Gerstmann-Straussler-Scheinker disease share antigenic determinants with those of Alzheimer disease
- (1990) Brain Res , vol.530 , pp. 325-329
- Giaccone, G.¹ Tagliavini, F.² Verga, L.³ Frangione, B.⁴ Farlow, M.R.⁵ Bugiani, O.⁶ Ghetti, B.⁷

12
- 0026644052
- An insert mutation in the chromosome 20 amyloid precursor gene in a Gerstmann-Straussler-Scheinker family
- (1992) J Neurol Sci , vol.111 , pp. 189-194
- Goldfarb, L.G.¹ Brown, P.² Vrboska, A.³ Baron, H.⁴ Mccombie, W.R.⁵ Cathala, F.⁶ Gibbs C.J., Jr.⁷ Gajdusek, D.C.⁸

13
- 0028990981
- The original Gerstmann-Straussler-Scheinker family of Austria: Divergent clinicopathological phanotypes but constant PrP genotypes
- (1995) Brain Pathol , vol.5 , pp. 201-211
- Heinfellner, J.A.¹ Brantner-Inthaler, S.² Cervenahova, L.³ Brown, P.⁴ Kitamoto, T.⁵ Tateishi, J.⁶ Diringer, H.⁷ Liberski, P.P.⁸ Regele, H.⁹ Feucht, M.¹⁰ Mayr, N.¹¹ Wessely, P.¹² Summer, K.¹³ Seitelberger, F.¹⁴ Budka, H.¹⁵

14
- 0028170720
- A variant of Gerstmann-Straussler-Scheinker disease carrying codon 105 mutation with codon 129 polymorphism of the prion protein gene: A clinicopathological study
- (1994) J Neurol Sci , vol.127 , pp. 77-86
- Itoh, Y.¹ Yamada, M.² Hayakawa, M.³ Shozawa, T.⁴ Tanaka, J.⁵ Matsushita, M.⁶ Kitamoto, T.⁷ Tateishi, J.⁸ Otomo, E.⁹

15
- 0001051781
- Distinctive PrP isoforms in Gerstmann-Straussler-Scheinker disease with tangles
- (1998) J Neuropathol Exp Neurol , vol.67 , pp. 517
- Lievens, P.M.J.¹ Quaglio, E.² Piccardo, P.³ Tranchant, C.⁴ Warter, J.M.⁵ Bird, T.⁶ Bugiani, O.⁷ Ghetti, B.⁸ Tagliavini, F.⁹

16
- 0008600872
- Coexistence of prion protein (PrP) amyloid, neurofibrillary tangles, and Lewy bodies in Gerstmann-Straussler-Scheinker disease with priori gene (PRNP) mutation F198S
- (1997) Brain Pathol , vol.7 , pp. 1379
- Mirra, S.¹ Young, K.² Gearing, M.³ Jones, R.⁴ Evatt, P.⁵ Piccardo, P.⁶ Ghetti, B.⁷

17
- 0032493453
- Different patterns of truncated prion protein fragments correlate with distinct phenotypes in P102L Gerstmann-Straussler-Scheinker disease
- (1998) Proc Natl Acad Sci USA , vol.95 , pp. 8322-8327
- Parchi, P.¹ Chen, S.G.² Brown, P.³ Zou, W.⁴ Capellari, S.⁵ Budka, H.⁶ Hainfellner, J.⁷ Reyes, P.F.⁸ Golden, G.T.⁹ Hauw, J.-J.¹⁰ Gajdusek, D.C.¹¹ Gambetti, P.¹²

18
- 0031754291
- Phenotypic variability of Gerstmann-Straussler-Scheinker disease is associated with prion protein heterogeneity
- (1998) J Neuropathol Exp Neurol , vol.57 , pp. 979-988
- Piccardo, P.¹ Dlouhy, S.R.² Lievens, P.M.J.³ Young, K.⁴ Bird, T.D.⁵ Nochlin, D.⁶ Dickson, D.W.⁷ Vinters, H.V.⁸ Zimmermann, T.R.⁹ Mackenzie, I.R.A.¹⁰ Kish, S.J.¹¹ Aug, L.-C.¹² De Carli, C.¹³ Pocchiari, M.¹⁴ Brown, P.¹⁵ Gibbs C.J., Jr.¹⁶ Gajdusek, D.C.¹⁷ Bugiani, O.¹⁸ Ironside, J.¹⁹ Tagliavini, F.²⁰ Ghetti, B.²¹ more..

19
- 73649154616
- Eigenartige familiar-hereditare Krankheit des Zentralnervensystems in einer niederosterreichischen Sippe
- (1962) Wien Klin Wochenschr , vol.74 , pp. 687-691
- Seitelberger, F.¹

20
- 0033528286
- Activation of microglial cells by PrP and β-amyloid fragments raises intracellular calcium through L-type voltage sensitive calcium channels
- (1999) Brain Res , vol.818 , pp. 168-170
- Silei, V.¹ Fabrizi, C.² Venturini, G.³ Salmona, M.⁴ Bugiani, O.⁵ Tagliavini, F.⁶ Lauro, G.M.⁷

21
- 0027174804
- A68 is a component of paired helical filaments in Gerstmann-Straussler-Scheinker disease, Indiana kindred
- (1993) Brain Res , vol.616 , pp. 325-328
- Tagliavini, F.¹ Giaccone, G.² Prelli, F.³ Verga, L.⁴ Porto, M.⁵ Frangione, B.⁶ Farlow, M.R.⁷ Ghetti, B.⁸ Bugiani, O.⁹

22
- 0008608121
- Prion diseases: PrP peptides, pathogenesis and treatment perspectives
- Harris DA, editor. Prions, molecular and cellular biology. Wymondham: Horizon Scientific Press
- (1999) , pp. 125-138
- Tagliavini, F.¹ Salmona, M.² Forloni, G.³ Malesani, P.⁴ Giaccone, G.⁵ Canciani, B.⁶ McArthur, R.⁷ Lansen, P.⁸ Piccardo, P.⁹ Dlouhy, S.R.¹⁰ Ghetti, B.¹¹ Frangione, B.¹² Prelli, F.¹³ Bugiani, O.¹⁴

23
- 0030011971
- Experimental transmission of Creutzfeldt-Jakob disease and related diseases in rodents
- (1996) Neurology , vol.46 , pp. 532-537
- Tateishi, J.¹ Kitamoto, T.² Hoque, M.Z.³ Furukawa, H.⁴

24
- 0030873721
- Neurofibrillary tangles in Gerstmann-Straussler-Scheinker syndrome with the A117V prion gene mutation
- (1997) J Neurol Neurosurg Psychiat , vol.63 , pp. 240-246
- Tranchant, C.¹ Sergeant, N.² Wattcz, A.³ Mohr, M.⁴ Warter, J.M.⁵ Delacourte, A.⁶

25
- 0001001586
- Gerstmann-Straussler-Scheinker disease (GSS) with a mutation at prion protein (PrP) residue 212
- (1998) J Neuropathol Exp Neurol , vol.57 , pp. 518
- Young, K.¹ Piccardo, P.² Kish, S.J.³ Aug, L.C.⁴ Dlouhy, S.⁵ Ghetti, B.⁶

26
- 0001612412
- The human genetic prion diseases
- Harris DA, editor. Prions, molecular and cellular biology. Wymondham: Horizon Scientific Press
- (1999) , pp. 139-175
- Young, K.¹ Piccardo, P.² Dlouhy, S.³ Bugiani, O.⁴ Tagliavini, F.⁵ Ghetti, B.⁶

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