메뉴 건너뛰기




Volumn 23, Issue 4, 2000, Pages 375-377

Upregulation of respiratory chain enzymes in guanidinoacetate methyltransferase deficiency

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE DIPHOSPHATE; ADENOSINE TRIPHOSPHATE; CREATINE; CREATINE PHOSPHATE; GUANIDINOACETIC ACID; METHYLTRANSFERASE; MITOCHONDRIAL ENZYME; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

EID: 0034041199     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005643617251     Document Type: Conference Paper
Times cited : (4)

References (9)
  • 1
    • 0032811447 scopus 로고    scopus 로고
    • Anomalies of mitochondrial ATP synthase regulation in four different types of neuronal ceroid lipofuscinosis
    • Das AM, Kohlschütter A (1999) Anomalies of mitochondrial ATP synthase regulation in four different types of neuronal ceroid lipofuscinosis. Mol Gen Metab 66: 349-355.
    • (1999) Mol Gen Metab , vol.66 , pp. 349-355
    • Das, A.M.1    Kohlschütter, A.2
  • 2
    • 0028108961 scopus 로고
    • ATP synthesis kinetic properties of mitochondria isolated from the rat extensor digitorum longus muscle depleted of creatine with β-guanidinopropionic acid
    • Freyssenet D, Berthon P, Geyssant A, Denis C (1994) ATP synthesis kinetic properties of mitochondria isolated from the rat extensor digitorum longus muscle depleted of creatine with β-guanidinopropionic acid. Biochim Biophys Acta 1186: 232-236.
    • (1994) Biochim Biophys Acta , vol.1186 , pp. 232-236
    • Freyssenet, D.1    Berthon, P.2    Geyssant, A.3    Denis, C.4
  • 3
    • 0016852667 scopus 로고
    • Tightly bound nucleotides of the energy transducing ATPase of chloroplasts and their role in photophosphorylation
    • Harris DA, Slater EC (1975) Tightly bound nucleotides of the energy transducing ATPase of chloroplasts and their role in photophosphorylation. Biochim Biophys Acta 387: 335-348.
    • (1975) Biochim Biophys Acta , vol.387 , pp. 335-348
    • Harris, D.A.1    Slater, E.C.2
  • 4
    • 13344255668 scopus 로고
    • Biomass and adenylate energy charge determination in microbial cell extracts and environmental samples
    • Hohn-Hansen O, Karl DM (1978) Biomass and adenylate energy charge determination in microbial cell extracts and environmental samples. Methods Enzymol 57: 73-85.
    • (1978) Methods Enzymol , vol.57 , pp. 73-85
    • Hohn-Hansen, O.1    Karl, D.M.2
  • 5
    • 0023836981 scopus 로고
    • The binding of the inhibitor protein is governed independently by ATP and membrane potential in ox-heart submitochondrial particles
    • Lippe G, Sorgato MC, Harris DA (1988). The binding of the inhibitor protein is governed independently by ATP and membrane potential in ox-heart submitochondrial particles. Biochim Biophys Acta 933: 12-21.
    • (1988) Biochim Biophys Acta , vol.933 , pp. 12-21
    • Lippe, G.1    Sorgato, M.C.2    Harris, D.A.3
  • 6
    • 0038376658 scopus 로고
    • Determination of creatine kinase isoenzymes in human serum by an immunological method using firefly luciferase
    • Lundin A (1978) Determination of creatine kinase isoenzymes in human serum by an immunological method using firefly luciferase. Methods Enzymol 57: 56-65.
    • (1978) Methods Enzymol , vol.57 , pp. 56-65
    • Lundin, A.1
  • 7
    • 0001477910 scopus 로고    scopus 로고
    • Differential effects of creatine depletion on the regulation of enzyme activities and on creatine-stimulated mitochondrial respiration in skeletal muscle, heart, and brain
    • O'Gorman E, Beutner G, Wallimann T, Brdiczka D (1996) Differential effects of creatine depletion on the regulation of enzyme activities and on creatine-stimulated mitochondrial respiration in skeletal muscle, heart, and brain. Biochim Biophys Acta 1276: 161-170.
    • (1996) Biochim Biophys Acta , vol.1276 , pp. 161-170
    • O'Gorman, E.1    Beutner, G.2    Wallimann, T.3    Brdiczka, D.4
  • 8
    • 0029959969 scopus 로고    scopus 로고
    • Guanidinoacetate methyltransferase deficiency: The first inborn error of creatine metabolism in man
    • Stöckler S, Isbrandt D, Hanefeld F, Schmidt B, von Figura K (1996) Guanidinoacetate methyltransferase deficiency: the first inborn error of creatine metabolism in man. Am J Hum Genet 58: 659-665.
    • (1996) Am J Hum Genet , vol.58 , pp. 659-665
    • Stöckler, S.1    Isbrandt, D.2    Hanefeld, F.3    Schmidt, B.4    Von Figura, K.5
  • 9
    • 0023804022 scopus 로고
    • The calcium-binding ATPase inhibitor protein from bovine heart mitochondria: Purification and properties
    • Yamada EW, Huzel NJ (1988) The calcium-binding ATPase inhibitor protein from bovine heart mitochondria: purification and properties. J Biol Chem 263: 11498-11503.
    • (1988) J Biol Chem , vol.263 , pp. 11498-11503
    • Yamada, E.W.1    Huzel, N.J.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.