Muscle membrane-skeleton protein changes and histopathological characterization of muscle-eye-brain disease

Neuromuscular Disorders

Volumn 10, Issue 1, 2000, Pages 16-23

  Auranen, M ^a,b   Rapola, J ^c   Pihko, H ^c   Haltia, M ^d   Leivo, I ^d   Soinila, S ^b   Virtanen, I ^a   Kalimo, H ^e   Anderson, L V B ^f   Santavuori, P ^c   Somer, H ^b  

^a UNIVERSITY OF HELSINKI   (Finland)

^b HELSINKI UNIVERSITY CENTRAL HOSPITAL   (Finland)

^c HELSINKI UNIVERSITY CENTRAL HOSPITAL   (Finland)

^d UNIVERSITY OF HELSINKI   (Finland)

^e TURKU UNIVERSITY HOSPITAL   (Finland)

^f NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

Basement membrane; Congenital muscular dystrophy; Histochemistry; Laminin; Merosin

Indexed keywords

ALPHA ACTININ; COLLAGEN TYPE 4; DESMIN; DYSTROGLYCAN; DYSTROPHIN; FIBRONECTIN; LAMININ; MUSCLE PROTEIN; SARCOGLYCAN; SPECTRIN;

ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CLINICAL TRIAL; DISEASE COURSE; FEMALE; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOREACTIVITY; INFANT; LIPID STORAGE; MALE; MEMBRANE STRUCTURE; MUSCLE BIOPSY; MUSCLE CELL; MUSCLE EYE BRAIN DISEASE; MUSCLE FIBER MEMBRANE; MUSCLE NECROSIS; MUSCULAR DYSTROPHY; PRIORITY JOURNAL; PROTEIN EXPRESSION; WESTERN BLOTTING;

ADOLESCENT; ADULT; AGED; BLOTTING, WESTERN; CYTOSKELETAL PROTEINS; DYSTROGLYCANS; DYSTROPHIN; FEMALE; HUMANS; IMMUNOHISTOCHEMISTRY; LAMININ; MALE; MEMBRANE GLYCOPROTEINS; MEMBRANE PROTEINS; MIDDLE AGED; MUSCLES; MUSCULAR DYSTROPHIES;

EID: 0033986951     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-8966(99)00066-8     Document Type: Article

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