Expanded CUG repeat RNAs form hairpins that activate the double-stranded RNA-dependent protein kinase PKR

RNA

Volumn 6, Issue 1, 2000, Pages 79-87

  Tian, Bin ^a   White, Robert J ^b   Xia, Tianbing ^b   Welle, Stephen ^b   Turner, Douglas H ^b   Mathews, Michael B ^a   Thornton, Charles A ^b,c  

^a RUTGERS NEW JERSEY MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF ROCHESTER SCHOOL OF MEDICINE AND DENTISTRY   (United States)

^c UNIVERSITY OF ROCHESTER MEDICAL CENTER   (United States)

Author keywords

CUG repeat; Double stranded RNA; dsRNA binding motif; Muscle; Myotonic dystrophy; PKR

Indexed keywords

DOUBLE STRANDED RNA; INTERFERON; PROTEIN KINASE;

ARTICLE; AUTOSOMAL DOMINANT DISORDER; ENZYME ACTIVATION; HUMAN; HUMAN CELL; MUSCULAR DYSTROPHY; MYOTONIC DYSTROPHY; NONHUMAN; PLASMID; PRIORITY JOURNAL; RNA BINDING; RNA SYNTHESIS; TRINUCLEOTIDE REPEAT;

BASE PAIRING; EIF-2 KINASE; ENDORIBONUCLEASES; ENZYME ACTIVATION; NUCLEIC ACID CONFORMATION; PROTEIN BINDING; RIBONUCLEASE III; RNA, DOUBLE-STRANDED; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 0033983537     PISSN: 13558382     EISSN: None     Source Type: Journal    
DOI: 10.1017/S1355838200991544     Document Type: Article

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