Hyperexcitability of cervical motor neurons during neck flexion in patients with Hirayama disease

Electromyography and Clinical Neurophysiology

Volumn 40, Issue 1, 2000, Pages 11-15

  Imai, T ^a   Shizukawa, H ^a   Nakanishi, K ^a   Kouge, N ^a   Hiura, K ^a   Kashiwagi, M ^a   Chiba, S ^a   Matsumoto, H ^a  

^a SAPPORO MEDICAL UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ADOLESCENT; ADULT; ARTICLE; CASE REPORT; CONTROLLED STUDY; DEVICE; EVOKED MUSCLE RESPONSE; EXCITABILITY; GRIP STRENGTH; HIRAYAMA DISEASE; HUMAN; MALE; NECK COLLAR; NECK MUSCLE; NEUROMUSCULAR FUNCTION; PARESIS; SPINAL MUSCULAR ATROPHY;

ADOLESCENT; ADULT; ANALYSIS OF VARIANCE; BRACES; ELECTROMYOGRAPHY; EVOKED POTENTIALS, MOTOR; FOLLOW-UP STUDIES; HAND; HAND STRENGTH; HUMANS; MAGNETICS; MALE; MOTOR NEURONS; MOVEMENT; MUSCLE WEAKNESS; NECK; NEURAL CONDUCTION; NEURAL PATHWAYS; SIGNAL PROCESSING, COMPUTER-ASSISTED; SPINAL MUSCULAR ATROPHIES OF CHILDHOOD; THUMB;

EID: 0033973957     PISSN: 0301150X     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (8)

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2. HIRAYAMA, K.: Non-progressive juvenile spinal muscular atrophy of the distal upper limb. In: Vinken, P. J., Bruyn, G. W. and Klawans, H. L. (eds.), Handbook of Clinical Neurology, Vol. 59. Elsevier Science Publishers, Amsterdam, 107-20, 1991.
3. IMAI, T., SAITO, M., MATSUMOTO, H., et al.: Correlation between the M and F wave characteristics and the innervated muscle strength in spinal muscular atrophy. Brain Dev., 20: 44-6, 1998.
4. KUWABARA, S., NAKAJIMA, M., TOKUMARU, Y. and HIRAYAMA, K.: Excitability of cervical lower motoneuron in juvenile muscular atrophy of the distal upper limb. Clin. Neurol., 34: 1111-5, 1994 (in Japanese with English abstract).
5. MISRA, U. K. and KALITA, J.: Central motor conduction in Hirayama disease. Electroenceph. clin. Neurophysiol., 97: 73-6, 1995.
6. ROBBERECHT, W., AGUIRRE, T., VAN DEN BOSCH, L. et al.: Familial juvenile focal amyotrophy of the upper extremity (Hirayama disease). Superoxide dismutase 1 genotype and activity. Arch. Neurol., 54: 46-50, 1997.
7. SOBUE, I., SAITO, N., IIDA, M. and ANDO, K.: Juvenile type of distal and segmental muscular atrophy of upper extremities. Ann. Neurol., 3: 429-32, 1978.
8. TOKUMARU, Y. and HIRAYAMA, K.: A cervical collar therapy for non-progressive juvenile spinal muscular atrophy of the distal upper limb (Hirayama's disease). Clin. Neurol., 32: 1102-6, 1992 (in Japanese with English abstract).