Secondary carnitine deficiency and impaired docosahexaenoic (22:6n-3) acid synthesis: A common denominator in the pathophysiology of diseases of oxidative phosphorylation and β-oxidation

FEBS Letters

Volumn 468, Issue 1, 2000, Pages 1-5

  Infante, Juan P ^a   Huszagh, Virginia A ^a  

^a Institute for Theoretical Biochemistry and Molecular Biology   (United States)

Author keywords

Acyl CoA dehydrogenase; Acylcarnitine; Adenine nucleotide translocator; Cardiomyopathy; Neuronal ceroid lipofuscinosis (Batten disease); Retinopathy

Indexed keywords

ACYLCARNITINE; ADENINE NUCLEOTIDE TRANSLOCASE; CARNITINE; PHOSPHOLIPID;

CARDIOMYOPATHY; CARNITINE DEFICIENCY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FATTY ACID OXIDATION; HUMAN; MITOCHONDRION; OXIDATIVE PHOSPHORYLATION; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RESPIRATORY CHAIN; RETINOPATHY; REVIEW;

ANIMALS; CARNITINE; DISEASE MODELS, ANIMAL; DOCOSAHEXAENOIC ACIDS; HUMANS; METABOLISM, INBORN ERRORS; MICE; MICE, KNOCKOUT; MITOCHONDRIA; MITOCHONDRIAL ENCEPHALOMYOPATHIES; NEURONAL CEROID-LIPOFUSCINOSES; OXIDATION-REDUCTION; OXIDATIVE PHOSPHORYLATION; PHOSPHOLIPIDS; VITAMIN E;

EID: 0033955887     PISSN: 00145793     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0014-5793(00)01083-8     Document Type: Review

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