Vascular complications of severe hyperhomocysteinemia in patients with homocystinuria due to cystathionine β-synthase deficiency: Effects of homocysteine-lowering therapy

Seminars in Thrombosis and Hemostasis

Volumn 26, Issue 3, 2000, Pages 335-340

  Yap, S ^a   Naughten, E R ^a   Wilcken, B ^a   Wilcken, D E L ^a   Boers, G H J ^a  

^a CHILDREN S UNIVERSITY HOSPITAL   (Ireland)

Author keywords

Cystathionine synthase deficiency; Effects of treatment; Homocystinuria; Severe hyperhomocysteinemia; Vascular complications

Indexed keywords

CYSTATHIONINE BETA SYNTHASE; HOMOCYSTEINE; PYRIDOXINE;

ABDOMINAL AORTA ANEURYSM; AMINO ACID BLOOD LEVEL; CARDIOVASCULAR RISK; DISEASE COURSE; DISEASE SEVERITY; ENZYME DEFICIENCY; HEART INFARCTION; HOMOCYSTINURIA; HUMAN; HYPERHOMOCYSTEINEMIA; LUNG EMBOLISM; PRIORITY JOURNAL; REVIEW; TREATMENT OUTCOME; VASCULAR DISEASE;

EID: 0033817657     PISSN: 00946176     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2000-8100     Document Type: Review

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