Malnutrition-associated rash of cystic fibrosis

Pediatric Dermatology

Volumn 17, Issue 5, 2000, Pages 337-347

  Darmstadt, G L ^a   McGuire, J ^a   Ziboh, V A ^a  

^a SEATTLE CHILDREN S RESEARCH INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ARACHIDONIC ACID; COPPER; ESSENTIAL FATTY ACID; FREE RADICAL; LINOLEIC ACID; M PROTEIN; PALMITIC ACID; PALMITOLEIC ACID; STEARIC ACID; ZINC;

ANTIOXIDANT ACTIVITY; ARTICLE; CASE REPORT; CONTROLLED STUDY; CYSTIC FIBROSIS; CYTOKINE PRODUCTION; DIFFERENTIAL DIAGNOSIS; DISEASE ASSOCIATION; FATTY ACID SYNTHESIS; FEMALE; HUMAN; HUMAN CELL; HUMAN TISSUE; INFANT; MALNUTRITION; PATHOGENESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; PROSTAGLANDIN METABOLISM; PROTEIN CALORIE MALNUTRITION; RASH;

CHILD, PRESCHOOL; CYSTIC FIBROSIS; DIAGNOSIS, DIFFERENTIAL; EXANTHEMA; FATTY ACIDS, ESSENTIAL; FEMALE; HUMANS; INFANT; PROTEIN-ENERGY MALNUTRITION; TREATMENT OUTCOME;

EID: 0033760766     PISSN: 07368046     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1525-1470.2000.017005337.x     Document Type: Article

References (139)

1. Essential fatty acid deficiency due to artificial diet in cystic fibrosis
2. Cystic fibrosis and malnutrition
3. Cystic fibrosis manifesting with acrodermatitis enteropathica-like eruption
4. Failure to thrive presenting with an unusual skin rash
5. Persistent morbidity and mortality of protein calorie malnutrition in young infants with cystic fibrosis
6. Dermatitis as a presenting sign of cystic fibrosis
7. Acrodermatite enteropathica-like in corso di mucoviscidosi
8. Acrodermatitis enteropathica-like rash in cystic fibrosis
9. Cystic fibrosis presenting as kwashiorkor with florid skin rash
10. Cystic fibrosis presenting with periorificial dermatitis
11. Cystic fibrosis and 'kwashiorkor
12. Clinical pathological conference
13. Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
14. The incidence of anemia, hypoproteinemia, and edema in infants as presenting symptoms of cystic fibrosis: A retrospective survey of the frequency of this symptom complex in 130 patients with cystic fibrosis
15. Hypoproteinemia and edema in infants with cystic fibrosis of the pancreas
16. Nutritional management of cystic fibrosis
17. Effect of linoleic acid intake on growth of infants with cystic fibrosis
18. Intestinal absorption of octanoic, decanoic, and linoleic acids: Effect of triglyceride structure
19. Absorption of triglycerides with defined or random structure by rats with biliary and pancreatic diversion
20. Dietary structured triacylglycerols containing docosahexanoic acid given from birth affect visual and auditory performance and tissue fatty acid profiles of rats
21. Ursodeoxycholic acid improves the hepatic metabolism of essential fatty acids and retinol in children with cystic fibrosis
22. The epidermal permeability barrier: Effects of physiologic and non-physiologic lipids
23. Topical ointment therapy benefits premature infants
24. Effects of repeated application of emollient cream to premature neonates' skin
25. The fatty acid composition of the serum chylomicrons and adipose tissue of children with cystic fibrosis
26. Essential fatty acids in cystic fibrosis
27. Abnormal levels of prostaglandins and fatty acids in blood of children with cystic fibrosis
28. Defective essential fatty acid metabolism in cystic fibrosis
29. Essential fatty acid status in cystic fibrosis and the effects of safflower oil supplementation
30. Two cases of cystic fibrosis in Japanese children: Studies on the essential fatty acid and prostaglandin metabolism
31. Fatty acid abnormalities in cystic fibrosis
32. Essential fatty acid status and fluidity of plasma phospholipids in cystic fibrosis infants
33. Essential fatty acid deficiency and predisposition to lung disease in cystic fibrosis
34. Abnormal fatty acid composition of plasma lipids in cystic fibrosis: A primary or secondary defect?
35. Essential fatty acid deficiency in well nourished young cystic fibrosis patients
36. Oral correction of essential fatty acid deficiency in cystic fibrosis
37. Supplemental calories improve essential fatty acid deficiency in cystic fibrosis patients
38. Long chain non-esterified fatty acid pattern in plasma of cystic fibrosis patients and their parents
39. Abnormal fatty acid turn-over in the phospholipids of the red blood cell membranes of the cystic fibrosis patients
40. Pathological regulation of arachidonic acid release in cystic fibrosis: The putative basic defect
41. Effect of essential fatty acid deficiency on the epidermal sphingolipids of the rat
42. Effects of essential fatty acid deficiency on epidermal O-acylsphingolipids and transepidermal water loss in young pigs
43. Pseudo-acylceramide with linoleic acid produces selective recovery of diminished cutaneous barrier function in essential fatty acid-deficient rats and has an inhibitory effect on epidermal hyperplasia
44. The biochemistry and function of stratum corneum lipids
45. Membrane structures in normal and essential fatty acid-deficient stratum corneum: Characterization by ruthenium tetroxide staining and x-ray diffraction
46. The permeability barrier in essential fatty acid deficiency: Evidence for a direct role for linoleic acid in barrier function
47. The mammalian cutaneous permeability barrier: Defective barrier function in essential fatty acid deficiency correlates with abnormal intercellular lipid disposition
48. Nutrition, aging, and the skin
49. Essential fatty acids and the skin
50. Direct transesterification of plasma fatty acids for the diagnosis of essential fatty acid deficiency in cystic fibrosis
51. Human essential fatty acid deficiency
52. New model of scaling dermatosis: Induction of hyperproliferation in hairless mice with eicosa-5, 8, 11-trienoic acid
53. Induction of epidermal hyperproliferation by topical n-3 polyunsaturated fatty acids on guinea pig skin linked to decreased levels of 13-hydroxyoctadecadienoic acid (13-HODE)
54. Nutritional modulation of guinea pig skin hyperproliferation by essential fatty acid deficiency is associated with selective down regulation of protein kinase C-β
55. Role of linoleic acid in infant nutrition
56. Alopecia and periorificial dermatitis in biotin-responsive multiple carboxylase deficiency
57. Skin manifestations of biotin deficiency
58. Biotin deficiency in an infant fed with amino acid formula and hypoallergenic rice
59. Acrodermatitis enteropathica
60. Zinc deficiency in two full term breast-fed infants
61. Transient zinc deficiency in a breast-fed premature infant
62. Acrodermatitis in breast-fed premature infants: Evidence of a defect of mammary zinc secretion
63. Symptomatic zinc deficiency in a one-year-old child precipitated by changing from formula to cow's milk
64. Acquired zinc deficiency in association with anorexia nervosa: Case report and review of the literature
65. Kwashiorkor-like zinc deficiency syndrome in anorexia nervosa
66. Trace metal and essential fatty acid deficiency during total parenteral nutrition
67. Interactions between zinc, essential fatty acids and prostaglandins: Relevance to acrodermatitis enteropathica, total parenteral nutrition, the glucagonoma syndrome, diabetes, anorexia nervosa and sickle cell anaemia
68. Nutritional deficiency and the skin
69. Effects of purified phytate and phytate-rich bread upon metabolism of zinc, calcium, phosphorus, and nitrogen in man
70. Skin changes in short-bowel syndrome
71. Acrodermatitis enteropathica-like syndrome in a dialysis patient
72. Childhood acquired immune deficiency syndrome manifesting as acrodermatitis enteropathica
73. Acrodermatitis enteropathica in a patient with the acquired immunodeficiency syndrome
74. Kwashiorkor/zinc deficiency overlap following partial gastrectomy
75. Skin in protein energy malnutrition
76. The plasma aminogram in kwashiorkor
77. Acrodermatitis enteropathica-like syndrome secondary to isoleucine deficiency during treatment of maple syrup urine disease
78. Periorificial dermatitis secondary to dietary deficiency of isoleucine in infants with maple syrup urine disease
79. Dermatitis in treated maple syrup urine disease
80. Exfoliative erythroderma resulting from inadequate intake of branched-chain amino acids in infants with maple syrup urine disease
81. Abnormal leucine/isoleucine ratio and acrodermatitis enteropathica-like rash in maple syrup urine disease (MSUD)
82. Acrodermatitis enteropathica-like eruption during treatment of maple syrup urine disease: Report of one case
83. Acrodermatitis enteropathica-like cutaneous lesions in organic aciduria
84. Acrodermatitis-like syndrome in organic aciduria
85. Cutaneous manifestations of methylmalonic acidemia
86. Organic acidemias
87. Unusual skin disorder during treatment of a baby with propionic acidemia
88. Acrodermatitis-like syndrome in organic aciduria
89. Cutaneous manifestations of methylmalonic and propionic acidaemia: A description based on 38 cases
90. Cutaneous lesions associated with isoleucine deficiency
91. Methylmalonic acidemia, cobalamin C type, presenting with cutaneous manifestations
92. Defective lysosomal release of vitamin B 12 (cb1F): A hereditary cobalamin metabolic disorder associated with sudden death
93. Parenteral nutrition in propionic and methylmalonic acidemia
94. Clinical heterogeneity in two patients with cb1F disease
95. Amino acid deficiency and skin rash associated with glucagonoma
96. Arginine deficiency syndrome: Its occurrence in carbamoyl phosphate synthetase deficiency
97. Arginine is an essential amino acid in a boy with deficiency of carbamoyl phosphate synthetase (CPS)
98. Neonatal citrullinemia with cutaneous manifestations and arginine deficiency
99. Neonatal citrullinemia: Treatment with ketoanalogues of essential amino acids
100. Acrodermatitis enteropathica-like lesions in amino acid deficiencies
101. Tyrosinemia with plantar and palmar keratosis and keratitis
102. Some problems in dietary amino acid requirements
103. The histidine requirement of the infant
104. The skin and nutritional disorders in the newborn
105. Skin breakdown in kwashiorkor responds to zinc
106. Zinc status and vitamin A transport in cystic fibrosis
107. Effects of albumin on fatty acid, protein, and eicosanoid levels in rat mesenteric arterial bed perfusions
108. Free radicals in the pathogenesis of kwashiorkor
109. The clinical manifestation of the kwashiorkor syndrome is related to increased lipid peroxidation
110. Leukotrienes in the pathophysiology of kwashiorkor
111. Actions of cytokines in relation to arachidonic acid metabolism and eicosanoid production
112. Calcium and potassium inhibit barrier recovery after disruption, independent of the type of insult in hairless mice
113. Integrity of the permeability barrier is crucial for maintenance of the epidermal calcium gradient
114. A role for ions in barrier recovery after acute perturbation
115. Control of growth and differentiation in vitro of human keratinocytes cultured in serum-free medium
116. The eocosanoids in biology and medicine
117. Correction of linoleic acid deficiency in cystic fibrosis
118. Relation between defective regulation of arachidonic acid release and symptoms in cystic fibrosis
119. Relationships among digital clubbing, disease severity, and serum prostaglandins F2α and E concentrations in cystic fibrosis patients
120. 2) metabolism?
121. Differential regulation of essential fatty acid metabolism to the prostaglandins: Possible basis for the interaction of zinc and copper in biological systems
122. Essential fatty acid status in zinc deficiency. Effect on lipid and fatty acid composition, desaturation activity and structure of microsomal membranes of rat liver and testes
123. Evidence that adverse effects of zinc deficiency on essential fatty acid composition in rats are in-dependent of food intake
124. Release of essential fatty acids from the rat mesenteric vascular bed perfused in vitro: Modulation by zinc
125. Maternal essential fatty acid supplementation increases zinc absorption in neonatal rats: Relevance to the defect in zinc absorption in acrodermatitis enteropathica
126. The nutritional and metabolic impact of gamma-linoleic acid on cats deprived of animal lipid
127. New model of a scaling dermatosis: Induction of hyperproliferation in hairless mice with eicosa-5, 8, 11-trienoic acid
128. 2 on rat skin: Inhibition of sterol ester biosynthesis and clearing of scaly lesions in essential fatty acid deficiency
129. Possible role of prostaglandins (PGs) in scaly dermatosis
130. Cutaneous barrier perturbation stimulates cytokine production in the epidermis of mice
131. Barrier function coordinately regulates epidermal IL-1 and IL-1 receptor antagonist mRNA levels
132. Normal mechanisms and pathophysiology of epidermal permeability barrier homeostasis
133. Occlusion lowers cytokine mRNA levels in essential fatty acid-deficient and normal mouse epidermis, but not after acute barrier disruption
134. Permeability barrier disruption alters the localization and expression of TNF alpha/protein in the epidermis
135. Barrier disruption increases gene expression of cytokines and the 55 kD TNF receptor in murine skin
136. Perturbation of epidermal barrier function correlates with initiation of cytokine cascade in human skin
137. Inflammatory skin disease in transgenic mice that express high levels of interleukin 1α in basal epidermis
138. IκBα deficiency results in a sustained NF-κB response and severe widespread dermatitis in mice
139. The diagnosis of cystic fibrosis: A consensus statement