Renal pathology and ultrastructural findings in Alport's syndrome

Renal Failure

Volumn 22, Issue 6, 2000, Pages 751-758

  Noel, L H ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN TYPE 4;

ALPORT SYNDROME; AUTOSOMAL RECESSIVE INHERITANCE; COLLAGEN DISEASE; CONFERENCE PAPER; GENE EXPRESSION; GLOMERULOSCLEROSIS; IMMUNOHISTOCHEMISTRY; KIDNEY DISEASE; KIDNEY DISTAL TUBULE; MICROSCOPY; PRIORITY JOURNAL; ULTRASTRUCTURE;

BASEMENT MEMBRANE; COLLAGEN; HUMANS; KIDNEY; KIDNEY GLOMERULUS; MICROSCOPY, ELECTRON; NEPHRITIS, HEREDITARY;

EID: 0033727929     PISSN: 0886022X     EISSN: None     Source Type: Journal    
DOI: 10.1081/JDI-100101960     Document Type: Conference Paper

References (28)

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13. Diagnosis of hereditary nephritis by failure of glomeruli to bind anti-glomerular basement membrane antibodies
14. Variability of GBM binding in hereditary nephritis
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16. Use of monoclonal antibody in differential diagnosis of children with hematuria and hereditary nephritis
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18. Localization of the Goodpasture epitope to a novel chain of basement membrane collagen
19. Nephritogenic antigen determinants in epidermal and renal basement membranes of kindreds with Alport-type familial nephritis
20. Molecular cloning of the human Goodpasture antigen demonstrates it to be the α 3 chain of type IV collagen
21. Differential expression of two basement membrane collagen genes. Co14A6 and Co14A5 demonstrated by immunofluorescence staining using peptide-specific monoclonal antibodies
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23. Type IV collagen α5 chain: Normal distribution and abnormalities in X-linked Alport syndrome revealed by monoclonal antibody
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