Congenital malformations of the ear and cochlear implantation in children: Review and temporal bone report of common cavity

Journal of Laryngology and Otology

Volumn 114, Issue SUPPL. 25, 2000, Pages 1-14

  Graham, John M ^a   Phelps, Peter D ^a   Michaels, Leslie ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

Acoustic nerve; Cerebrospinal fluid; Cochlea; Cochlear implant; Facial nerve; Fistula; Malformations; Temporal bone

Indexed keywords

CEREBROSPINAL FLUID FISTULA; COCHLEA PROSTHESIS; COCHLEAR NERVE; CONGENITAL MALFORMATION; DIAGNOSTIC IMAGING; EAR MALFORMATION; FACIAL NERVE; HUMAN; IMPLANTATION; KLIPPEL FEIL SYNDROME; MICROTIA; NERVE STIMULATION; PERCEPTION DEAFNESS; PERILYMPH; REVIEW; TEMPORAL BONE; ADOLESCENT; ADULT; CHILD; COCHLEA; CRANIOFACIAL MALFORMATION; EAR; EXTERNAL EAR; FEMALE; FISTULA; HEARING DISORDER; INNER EAR; INNERVATION; MALE; METHODOLOGY; MIDDLE EAR; PATHOLOGY; PATHOPHYSIOLOGY; PEROPERATIVE COMPLICATION; PRENATAL DEVELOPMENT; PRESCHOOL CHILD; TREATMENT OUTCOME;

ADOLESCENT; ADULT; CHILD; CHILD, PRESCHOOL; COCHLEA; COCHLEAR IMPLANTATION; COCHLEAR IMPLANTS; CRANIOFACIAL ABNORMALITIES; EAR; EAR, EXTERNAL; EAR, INNER; EAR, MIDDLE; FACIAL NERVE; FEMALE; FISTULA; HEARING DISORDERS; HUMANS; INTRAOPERATIVE COMPLICATIONS; MALE; TEMPORAL BONE; TREATMENT OUTCOME;

EID: 0033649949     PISSN: 00222151     EISSN: None     Source Type: Journal    
DOI: 10.1258/0022215001904842     Document Type: Review

References (62)

1. Altmann F. Malformation of the auricle and external auditory meatus. Arch Otolarygol 1995;54:115-39
2. Nager GT. Congenital aural atresia: anatomy and surgical management. Birth Defects 1971;4:33-51
3. Cremers CWRJ, Oudenhoven JMTM, Marres EHMA. Congenital aural atresia. A new subclassification and surgical management. Clin Otolaryngol 1984;9:119-27
4. Mondini C. Anatomica surdi nati sectio. Bononiensi scientarium et artium instituto atqu academia commentarii Bononiae 1791;7:419-28
5. Richards SH, Gibbin KP. Recurrent meningitis due to congenital fistula of stapedial footplate. J Laryngol Otol 1977;91:1063-71
6. Phelps PD, King A, Michaels L. Cochlear dysplasia and meningitis. Am J Otol 1994;15:551-7
7. Jackler RK, Luxford WM, House WF. Congenital malformations of the inner ear: a classification based on embryonogenesis. Laryngoscope 1987;97(suppl 4):2-14
8. Streeter GL. On the development of the membranous labyrinth and the acoustic and facial nerves in the human embryo. Am J Anat 1906;6:139
9. Phelps PD. Ear dysplasia after Mondini. J Laryngol Otol 1994;108:461-5
10. Schuknecht HF. Mondini dysplasia, a clinical and pathological study. Ann Otol Rhinol Laryngol 1980;89(suppl 65):1-10
11. Paparella MM. Mondini's deafness, a review of histopathology. Ann Otol Rhinol Laryngol 1980; 67(suppl 65):1-10
12. Cock E. The pathology of congenital deafness. Guy's Hospital Reports 1838;7:289-307
13. Phelps PD, Michaels L. The common cavity congenital deformity of the inner ear. ORL 1995;57:228-31
14. Triglia JM, Nicollas R, Ternier F, Cannoni M. Les surdites par malformation de l'oreille interne. Ann Otolaryngol Chir Cervicofac 1993;110:241-6
15. Smith SO, Harker LA. Single gene influences on radiologically-detectable malformations of the inner ear. J Commun Disord 1998;31:391-410
16. Phelps PD, Lloyd GAS. Diagnostic Imaging of the Ear, 2nd edn. London: Springer-Verlag, 1990
17. Casselman JW, Kuhweide R, Deimling M, Ampe W, DeHaene I, Meeus L Constructive interference in steady state-2DFT MR imaging of the inner ear and cerebellopontine angle. Am J Neuroradiol 1993;14:47-57
18. Goldenhar M. Associations malformatives de l'oeil et de l'oreille, en particulier le syndrome dermoide epibulbaire-appendices audiculaires-fistula auris congenita et ses relations avec la dysostose mandibulo-faciale. J Genet Hum 1952;1:243-82
19. Franceschatti PA, Zwahlen P. Un syndrome nouveau: la dysostose mandibulofaciale. Bull Schweiz. Akad Med Wiss 1994;1:60-6
20. Klippel M, Feil A. Un cas d'absence des vertebres cervicales avec cage thoracique remontant jusqu'a la base du crane (cage thoracique cervicale). Nouv Iconogr Salpet 1912;25:223-50
21. Nager FR, Reynier JP. Das Gehororgan bei den augeborenen Kopfmissbildung. Pract Otorhinolaryngol 1948;10 (suppl 2):1
22. Windle-Taylor PC, Emery PJ, Phelps PD. Ear deformities associated with the Klippel-Feil syndrome. Ann Otol Rhinol Laryngol 1981;90:210-6
23. Proops DW. The Birmingham bone anchored hearing aid programme: surgical methods and complications. J Laryngol Otol 110(suppl 21): 7-12
24. Livingstone OH. The establishment of sound conduction in congenital deformities of the external ear. J Laryngol Otol 1959;73:231-41
25. Hoffman RA, Downey LL, Waltzman SB, Cohen NL. Cochlear implantation in children with cochlear malformations. Am J Otol 1997;18:184-7
26. Luntz M, Balkany T, Hodges AV, Telischi FF. Cochlear implants in children with congenital inner ear malformations. Arch Otolaryngol Head Neck Surg 1998;123:974-7
27. Weber BP, Dillo W, Dietrich B, Maneke I, Bertram B, Lenarz T. Paediatric cochlear implantation in cochlear malformations. Am J Otol 1998;19:747-53
28. Molter DW, Pate BR, McElveen JT. Cochlear implantation in the congenitally malformed ear. Otolaryngol Head Neck Surg 1993;108:174-7
29. McElveen JT, Carrasco VN, Miyamoto RT, Linthicum FH. Cochlear implantation in common cavity malformations using a transmastoid labyrnthotomy approach. Laryngoscope 1997;107:1032-6
30. Tucci DL, Telian SA, Zimmerman-Phillips S, Zwolen TA, Kileny PR. Cochlear implantation in patients with cochlear malformations. Arch Otolaryngol Head Neck Surg 1995; 121:833-8
31. Slattery WH, Luxford WM. Cochlear implantation in the congenital deformed cochlea. Laryngoscope 1995;105: 1184-7
32. Janssens S, Govaerts PJ, Cassehnan J, Van Rompaey W, Van Langenhove A, Somers T, et al. The LAURA multichannel cochlear implant in a true Mondini dysplasia. Eur Arch Otorhinolaryngol 1996;253:301-4
33. Temple RH, Ramsden RT, Axon PR, Saeed SR. The large vestibular aqueduct syndrome: the role of cochlear implantation in its management. Clin Otolaryngol 1999;24:301-6
34. Au G, Gibson W. Cochlear implantation in children with large vestibular aqueduct syndrome. Am J Otol 1999;20: 183-6
35. Lemmerling MM, Mancuso AA, Antonelli PJ, Kubilis PS. Normal modiolus: CT appearance in patients with a large vestibular aqueduct. Radiology 1997;204:213-9
36. Weber BP, Lenarz T, Dillo W, Maneke I, Bertram B. Malformations in cochlear implant patients. Am J Otol 1997;18:S64-5
37. Graham JM, Ashcroft P. Direct measurement of CSF pressure through the cochlea in a congenitally deaf child with Mondini dysplasia undergoing cochlear implantation. Am J Otol 1999;20:205-8
38. Nelson, Textbook of Paediatrics, 13th edn. Philadelphia: W. B. Saunders, 1987
39. Page EL, Eby TL. Meningitis after cochlear implantation in Mondini malformation. Otolaryngol Head Neck Surg 1997;16:104-6.32
40. Fisch U. Tympanoplasty, Mastoidectomy and Stapes Surgery. New York: Theime, 1994
41. Bendet E, Cerenko D, Linder TB, Fisch U. Cochlear implantation after subtotal petrosectomies. Eur Arch Otorhinolaryngol 1998;255:169-74
42. Schmidt JM. Cochlear neuronal populations in developmental defects of the inner ear: implications for cochlear implantation. Acta Otolaryngol 1985;99:14-20
43. Linthicum FH, Fayad J, Otto S, Galey FR, House W. Inner ear morphological changes resulting from cochlear implantation. Am J Otol 1991;12(suppl):8-10
44. Steel K, Bock GR. Electrically-evoked responses in animals with progressive spiral ganglion degeneration. Hear Res 1984;15:59-67
45. Smith L, Simmons FB. Estimating eighth nerve survival by electrical stimulation. Ann Otol Rhinol Laryngol 1983;92: 19-23
46. Hartshorn DO, Miller JM, Altschuler A. Protective effect of electrical stimulation in the deafened guinea-pig cochlea. Otolaryngol Head Neck Surg 1991;104:311-9
47. French ML. Electrical impedance measurements with the CI24 for a child with Mondini dysplasia. Br J Audiol 1999;33:61-6
48. Jackler RK, Luxford WM, House WF. Sound detection with the cochlear implant in five ears of four children with congenital malformations of the cochlea. Laryngoscope 1987;97(suppl 4):15-7
49. Gray RF, Ray J, Baguley DM, Vanat Z, Begg J, Phelps PD. Cochlear implant failure due to unexpected absent eighth nerve - a cautionary tale. J Laryngol Otol 1983;112:646-9
50. Graham JM, East CA, Fraser JG. UCH/RNID single channel cochlear implant: surgical technique. J Laryngol Otol 1989;(suppl 18):14-9
51. Niparko JK, Oviatt DL, Coker NJ, Sutton L, Waltzman SB, Cohen NL. Facial nerve stimulation with cochlear implantation. Otolaryngol Head Neck Surg 1991;104:826-30
52. Shea JJ, Domico EH. Facial nerve stimulation after successful cochlear implantation. Am J Otol 1994;15:752-6
53. Muckle RP, Levine SC. Facial nerve stimulation produced by cochlear implants in patients with cochlear otosclerosis. Am J Otol 1994;15:394-8
54. Weber BP, Lenarz T, Battmer RD, Hartrampf R, Dahm MC, Dietrich B. Otosclerosis and facial nerve stimulation. Ann Otol Rhinol Laryngol 1995;104(suppl):445-7
55. Kelsall DC, Shallop JK, Brammeier TG, Prenger EC. Facial nerve stimulation after Nucleus 22-channel cochlear implantation. Am J Otol 1997;18:336-41
56. Ramsden R, Bance M, Giles E, Mawman D. Cochlear otosclerosis: a unique positioning and programming problem. J Laryngol Otol 1997;111:262-5
57. Cohen NL, Hoffman RA, Stroschein M. Medical or surgical complications related to the Nucleus multichannel cochlear implant. Ann Otol Rhinol Laryngol 1988;97:8-13
58. Miyamoto RT, McConkey Robbins AJ, Myres WA, Pope ML. Cochlear implantation in the Mondini inner ear malformation. Am J Otol 1986;7:258-61
59. Silverstein H, Smouha E, Morgan N. Multichannel cochlear implantation in a patient with bilateral Mondini deformities. Am J Otol 1988;9:451-5
60. Firszt JB, Reder RM, Novak MA. Multichannel cochlear implantation with inner ear malformation: case report of performance and management. J Am Acad Audiol 1995; 6:235-42
61. Dahm MC, Weber BP. Cochlear implantation in a Mondini malformation of the inner ear and the management of perilymphatic gusher. Adv Otorhinolaryngol 1995;50:66-71
62. Munro KJ, George CR, Haake NP. Audiological changes after multichannel cochlear implantation in patients with Mondini dysplasia. Br J Audiol 1996;30:369-79