Disruption of disulfide bonds is responsible for impaired secretion in human complement factor H deficiency

Journal of Biological Chemistry

Volumn 274, Issue 17, 1999, Pages 11782-11788

  Schmidt, Bela Z ^a   Fowler, Natalie L ^a   Hidvegi, Tunde ^a   Perlmutter, David H ^a,b   Colten, Harvey R ^a,c  

^a ST LOUIS CHILDREN S HOSPITAL   (United States)

^b WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^c NORTHWESTERN UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENT FACTOR H;

AMINO ACID SUBSTITUTION; ANIMAL CELL; ARTICLE; COMPLEMENT ACTIVATION; COMPLEMENT DEFICIENCY; CONTROLLED STUDY; DISULFIDE BOND; HUMAN; HUMAN CELL; NONHUMAN; NUCLEOTIDE SEQUENCE; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; SITE DIRECTED MUTAGENESIS;

ANIMALS; BASE SEQUENCE; CELL LINE; COMPLEMENT FACTOR H; COS CELLS; DISULFIDES; DNA PRIMERS; HUMANS; KINETICS; MUTAGENESIS, SITE-DIRECTED; TRANSFECTION;

EID: 0033597315     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.274.17.11782     Document Type: Article

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