Folding and assembly of type X collagen mutants that cause metaphyseal chondrodysplasia-type schmid: Evidence for co-assembly of the mutant and wild-type chains and binding to molecular chaperones

Journal of Biological Chemistry

Volumn 274, Issue 11, 1999, Pages 7570-7575

  McLaughlin, Stephen H ^a,b   Conn, Shanti N ^a   Bulleid, Neil J ^a  

^a UNIVERSITY OF MANCHESTER   (United Kingdom)

^b UNIVERSITY OF CAMBRIDGE   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN TYPE 10;

ARTICLE; CARBOXY TERMINAL SEQUENCE; CHONDRODYSPLASIA; COLLAGEN SYNTHESIS; GENE MUTATION; GROWTH PLATE; HUMAN; HUMAN CELL; METAPHYSIS; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN STABILITY;

ANIMALS; BASE SEQUENCE; BIOPOLYMERS; CATTLE; CELL LINE; COLLAGEN; DNA PRIMERS; HUMANS; MOLECULAR CHAPERONES; MUTAGENESIS, SITE-DIRECTED; OSTEOCHONDRODYSPLASIAS; PROTEIN BINDING; PROTEIN FOLDING;

BOVINAE;

EID: 0033548550     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.274.11.7570     Document Type: Article

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