Adult Leigh syndrome: Treatment with intravenous soybean oil for acute central respiratory failure

European Journal of Neurology

Volumn 6, Issue 5, 1999, Pages 613-615

  Kumagai, Rumi ^a,b   Ichikawa, Keiji ^a   Yasui, Takashi ^a   Kageyama, Yasufumi ^a   Miyabayashi, Shigeaki ^c  

^a Hyogo Prefectural Amagasaki Hospital   (Japan)

^b HIROSHIMA UNIV SCHOOL OF MEDICINE   (Japan)

^c NONE

Author keywords

Ketogenic therapy; Leigh syndrome; Pyruvate dehydrogenase complex deficiency; Soybean oil; Treatment

Indexed keywords

ANTICONVULSIVE AGENT; BIOTIN; CHOLINERGIC RECEPTOR BLOCKING AGENT; LEVODOPA; LIPID EMULSION; PENTOBARBITAL; PYRUVATE DEHYDROGENASE COMPLEX; SOYBEAN OIL; STEROID; THIAMINE;

ADULT; ARTICLE; CASE REPORT; DIET THERAPY; DIPLOPIA; DYSTONIA; FEMALE; HUMAN; KETOGENESIS; LACTIC ACIDOSIS; LEIGH DISEASE; PRIORITY JOURNAL; PYRUVATE DEHYDROGENASE COMPLEX DEFICIENCY; RESPIRATORY FAILURE; UNCONSCIOUSNESS; VISUAL IMPAIRMENT;

EID: 0033397750     PISSN: 13515101     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1468-1331.1999.650613.x     Document Type: Article

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