Therapy of metabolic disorders with intravenous (IV) access ports and long term intravenous L-carnitine therapy

Southeast Asian Journal of Tropical Medicine and Public Health

Volumn 30, Issue SUPPL. 2, 1999, Pages 152-153

  Winter, Susan ^a   Birek, Laura ^a   Walker, Ty ^a   Phalin Roque, Judy ^a   Chandler, Mary Jane ^a   Field, Cheryl ^a   Zorn, Elinor ^a  

^a Valley Children s Hospital   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CARNITINE; METHYLMALONIC ACID; PROPIONIC ACID DERIVATIVE;

ARTICLE; FEMALE; HUMAN; INBORN ERROR OF METABOLISM; INDWELLING CATHETER; INTRAVENOUS DRUG ADMINISTRATION; URINE;

CARNITINE; CATHETERS, INDWELLING; FEMALE; HUMANS; INFUSIONS, INTRAVENOUS; METABOLISM, INBORN ERRORS; METHYLMALONIC ACID; PROPIONIC ACIDS;

EID: 0033302185     PISSN: 01251562     EISSN: 26975718     Source Type: Journal    
DOI: None     Document Type: Article

References (6)

1. Bohles H, et al. The effect of intravenous L-carnitine on propionic acid excretion in acute propionic acidemia. Eur J Pediatr 1984;143: 61-3.
2. Itoh T, et al. Effect of carnitine administration on glycine metabolism in patients with isovaleric acidemia: significance of acetylcarnitine determination to estimate the proper carnitine dose. Tohoku J Exp Med 1996, 179: 101-9.
3. Penn D, et al. Carnitine in the treatment of methylmalonic aciduria. Monatsschr Kinderheilkd. 1986; 134: 758-61.
4. Roe CR, et al. Carnitine homeostasis in the organic acidurias. Prog Clin Biol Res 1990; 321: 383-402.
5. VanHove JL, et al. Intravenous L-carnitine and acctylL-carnitine in medium-chain acyl-CoA-enzyme dehydrogenase deficiency and isovaleric acidemia. Pediatr Res 1994; 35: 96-101.
6. Winter S, Buist N. Clinical treatment guide to inborn errors of metabolism 1998. J Rare Dis 1998; IV: 18-46.