Syncope and Inducible Ventricular Fibrillation in a Woman with Hemochromatosis

Journal of Interventional Cardiac Electrophysiology

Volumn 3, Issue 3, 1999, Pages 225-229

  Strobel, John S ^a   Fuisz, Anthon R ^a   Epstein, Andrew E ^a   Plumb, Vance J ^a  

^a University of Alabama at Birmingham and Birmingham Veterans Affairs Medical Center   (United States)

Author keywords

Electrophysiologic study; Hemochromatosis; Nuclear magnetic resonance imaging; Polymorphic ventricular tachycardia; Syncope; Ventricular fibrillation

Indexed keywords

DIAGNOSTIC AGENT;

ARTICLE; CARDIOVERSION; CASE REPORT; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAPHY; EXERCISE TEST; FEMALE; HEART MUSCLE; HEART VENTRICLE FIBRILLATION; HEMOCHROMATOSIS; HUMAN; MIDDLE AGED; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PATHOLOGY; PATHOPHYSIOLOGY; RECURRENT DISEASE; SYNCOPE;

ECHOCARDIOGRAPHY; ELECTRIC COUNTERSHOCK; ELECTROCARDIOGRAPHY, AMBULATORY; EXERCISE TEST; FEMALE; HEMOCHROMATOSIS; HUMANS; MAGNETIC RESONANCE SPECTROSCOPY; MIDDLE AGED; MYOCARDIUM; RECURRENCE; SYNCOPE; VENTRICULAR FIBRILLATION;

EID: 0033210883     PISSN: 1383875X     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1009891406964     Document Type: Article

References (18)

1. Wang T-L, Wen-Jone C, Liau C-S, et al. Sick sinus syndrome as the early manifestation of cardiac hemochromatosis. J Electrocardiol 1994;27:91-95.
2. Schellhammer PF, Engle MA, Hagstrom JWC. Histochemical studies of the myocardium and conduction system in acquired iron-storage disease. Circulation 1967;35:631-637.
3. Buja LM, Roberts WC. Iron in the heart: Etiology and clinical significance. Am J Med 1971;51:209-221.
4. Vigorita VJ, Hutchins GM. Cardiac conduction system in hemochromatosis: Clinical and pathologic features of six patients. Am J Cardiol 1979;44:418-423.
5. Rosenqvist M, Hultcrantz R. Prevalence of a haemochromatosis among men with clinically significant bradyarrhythmias. Eur Heart J 1989;10:473-478.
6. Short EM, Winkle RA, Billingham ME. Myocardial involvement in idiopathic hemochromatosis: morphologic and clinical improvement following venesection. Am J Med 1981;70: 1275-1279.
7. Yalçinkaya S, Kumbasar D, Semiz E, et al. Sustained ventricular tachycardia in cardiac hemochromatosis treated with amiodarone. J Electrocardiol 1997;30:147-149.
8. Edwards CQ, Griffen LM, Goldgar D, et al. Prevalence of hemochromatosis among 11,065 presumably healthy blood donors. N Eng J Med 1988;318:1355-1362.
9. Leggett BA, Halliday JW, Brown NN, et al. Prevalence of hemochromatosis among asymptomatic Australians. Br J Haematol 1990;74:525-530.
10. Simon M, Bourel M, Fauchet R, et al. Association of HLA-A3 and HLA-B14 antigens with idiopathic haemochromatosis. Gut 1976;17:332-334.
11. Edwards CQ, Dadone MM, Skolnick MH, et al. Hereditary haemochromatosis. Clin Haematol 1982;11:411-435.
12. Feder JN, Gnirke A, Thomas W, et al. A novel MHC class I-like gene is mutated in patients with hereditary haemochromatosis. Nat Genet 1996;13:399-408.
13. Cartwright GE, Edwards CQ, Kravitz K, et al. Hereditary hemochromatosis: Phenotypic expression of the disease. N Eng J Med 1979;301:175-179.
14. Olson LJ, Edwards WD, McCall JT. Cardiac iron deposition in idiopathic hemochromatosis: Histologic and analytic assessment of 14 hearts from autopsy. J Am Coll Cardiol 1987;10:1239-1243.
15. Dabestani A, Child AS, Henze E, et al. Primary hemochromatosis: Anatomic and physiologic characteristics of the cardiac ventricles and their response to phelbotomy. Am J Cardiol 1984;54:153-159.
16. James TN. Pathology of the cardiac conduction system in hemochromatosis. N Eng J Med 1964:271:92-94.
17. Finch SC, Finch CA. Idiopathic hemochromatosis, an iron storage disease. Medicine 1955:34:381-430.
18. Olson LJ, Edwards WD, Holmes DR Jr, et al. Endomyocardial biopsy in hemochromatosis: Clinicopathologic correlates in six cases. J Am Coll Cardiol 1989;13: 116-120.