Processing of normal lysosomal and mutant N-acetylgalactosamine 4-sulphatase: BiP (immunoglobulin heavy-chain binding protein) may interact with critical protein contact sites

Biochemical Journal

Volumn 341, Issue 1, 1999, Pages 193-201

  Bradford, Tessa M ^a   Gething, Mary Jane ^b   Davey, Richard ^a   Hopwood, John J ^a   Brooks, Doug A ^a  

^a WOMEN S AND CHILDREN S HOSPITAL   (Australia)

^b UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

Endoplasmic reticulum; Molecular chaperones; Mutant protein; Protein conformation; Protein processing

Indexed keywords

CHAPERONE; GLUCOSE REGULATED PROTEIN; GLYCOSYLATED PROTEIN; LYSOSOME ENZYME; MANNOSE 6 PHOSPHATE; MUTANT PROTEIN; N ACETYLGALACTOSAMINE 4 SULFATASE;

ANIMAL CELL; ARTICLE; CONFORMATIONAL TRANSITION; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; ENZYME CONFORMATION; ENZYME SYNTHESIS; LYSOSOME; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN PROCESSING; PROTEIN PROTEIN INTERACTION; PROTEIN TRANSPORT; SITE DIRECTED MUTAGENESIS;

BINDING SITES; BIOLOGICAL TRANSPORT; CARRIER PROTEINS; CATALYTIC DOMAIN; CELL COMPARTMENTATION; CYSTEINE; ENDOPLASMIC RETICULUM, ROUGH; HEAT-SHOCK PROTEINS; HUMANS; LYSOSOMES; MICROSCOPY, IMMUNOELECTRON; MODELS, MOLECULAR; MOLECULAR CHAPERONES; MUTAGENESIS, SITE-DIRECTED; MUTATION; N-ACETYLGALACTOSAMINE-4-SULFATASE; PROTEIN BINDING; PROTEIN FOLDING; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN STRUCTURE, SECONDARY; THREONINE; VACUOLES;

ANIMALIA;

EID: 0033166502     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/0264-6021:3410193     Document Type: Article

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