Determination of total fatty acids in plasma: cis-5-tetradecenoic acid (C(14:1)ω-9) in the diagnosis of long-chain fatty acid oxidation defects

Journal of Inherited Metabolic Disease

Volumn 22, Issue 3, 1999, Pages 286-288

  Divry, P ^a   Vianey Saban, C ^a   Mathieu, M ^a  

^a HÔPITAL DEBROUSSE   (France)

Author keywords

[No Author keywords available]

Indexed keywords

LONG CHAIN FATTY ACID;

CLINICAL ARTICLE; CONFERENCE PAPER; CONTROLLED STUDY; FATTY ACID OXIDATION; HUMAN; METABOLIC DISORDER;

3-HYDROXYACYL COA DEHYDROGENASES; ACYL-COA DEHYDROGENASE; ACYL-COA DEHYDROGENASE, LONG-CHAIN; CHILD; FATTY ACID DESATURASES; FATTY ACIDS; FATTY ACIDS, MONOUNSATURATED; HUMANS; LIPID METABOLISM, INBORN ERRORS;

EID: 0033038554     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005567030040     Document Type: Conference Paper

References (5)

1. Costa CG, Dorland L, Holwerda U, et al (1998) Simultaneous analysis of plasma free fatty acids and their 3-hydroxy analogs in fatty acid β-oxidation disorders. Clin Chem 44: 463-471.
2. Lepage G, Roy CC (1986) Direct transesterification of all classes of lipids in a one-step reaction. J Lipid Res 27: 114-120.
3. Lepage G, Roy CC (1988) Specific methylation of plasma nonesterified fatty acids in a one-step reaction. J Lipid Res 29: 227-235.
4. Martinez G, Jimenez-Sanchez G, Divry P, et al (1997) Plasma free fatty acids in mitochondrial fatty acid oxidation defects. Clin Chim Acta 267: 143-154.
5. Onkenhout W, Venizelos V, Van der Poel PFH, et al (1995) Identification and quantification of intermediates of unsaturated fatty acid metabolism in plasma of patients with fatty acid oxidation disorders. Clin Chem 41: 1467-1474.