Intracellular degradation of fluorescent glycolipids by lysosomal enzymes and their activators

Journal of Inherited Metabolic Disease

Volumn 22, Issue 5, 1999, Pages 623-637

  Madar Shapiro, L ^a   Pasmanik Chor, M ^a   Dinur, T ^b   Dagan, A ^b   Gatt, S ^b   Horowitz, M ^a  

^a TEL AVIV UNIVERSITY   (Israel)

^b HEBREW UNIVERSITY OF JERUSALEM   (Israel)

Author keywords

[No Author keywords available]

Indexed keywords

CERAMIDE; CEREBROSIDE SULFATASE; ENZYME ACTIVATOR; FLUORESCENT DYE; GLUCOSYLCERAMIDE; GLYCOLIPID; LYSOSOME ENZYME; PROSAPOSIN; SPHINGOLIPID ACTIVATOR PROTEIN;

ARTICLE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; ENDOCYTOSIS; ENZYME ACTIVITY; GAUCHER DISEASE; GENE MUTATION; HUMAN; HUMAN CELL; HYDROLYSIS; LIPID TRANSPORT; LYSOSOME; NORMAL HUMAN; PROTEIN DEFICIENCY; SKIN FIBROBLAST;

CEREBROSIDE-SULFATASE; ENZYME ACTIVATION; FLUORESCENT DYES; GAUCHER DISEASE; GLUCOSYLCERAMIDASE; GLUCOSYLCERAMIDES; GLYCOPROTEINS; HUMANS; INTRACELLULAR FLUID; LYSOSOMES; MUTATION; RHODAMINES; SAPOSINS; SPHINGOLIPID ACTIVATOR PROTEINS; SULFOGLYCOSPHINGOLIPIDS;

EID: 0032997392     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005573812430     Document Type: Article

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