-
1
-
-
0002314552
-
Cystic fibrosis
-
Scriver CR, Beaudet AL, Sly WS, Valle D, eds. New York, McGraw-Hill
-
Boat TF, Welsh MJ, Beaudet AL. Cystic fibrosis. In: Scriver CR, Beaudet AL, Sly WS, Valle D, eds. The Metabolic Basis of Inherited Disease. New York, McGraw-Hill, 1989; pp. 2649-2680.
-
(1989)
The Metabolic Basis of Inherited Disease
, pp. 2649-2680
-
-
Boat, T.F.1
Welsh, M.J.2
Beaudet, A.L.3
-
2
-
-
0028101526
-
Pathophysiology of pulmonary disease in cystic fibrosis
-
Petty TL, Cherniack RM, Fiel SB, eds. New York and Stuttgart, Thieme Medical Publishers
-
Marshall BC. Pathophysiology of pulmonary disease in cystic fibrosis. In: Petty TL, Cherniack RM, Fiel SB, eds. Seminars in Respiratory and Critical Care Medicine: Vol. 15; Cystic Fibrosis. New York and Stuttgart, Thieme Medical Publishers, 1994; pp. 364-374.
-
(1994)
Seminars in Respiratory and Critical Care Medicine: Vol. 15; Cystic Fibrosis
, vol.15
, pp. 364-374
-
-
Marshall, B.C.1
-
3
-
-
0028040989
-
The ageing cystic fibrosis patient: Presentations and problems
-
Petty TL, Cherniack RM, Fiel SB, eds. New York and Stuttgart, Thieme Medical Publishers
-
Burke W, Aitken ML. The ageing cystic fibrosis patient: presentations and problems. In: Petty TL, Cherniack RM, Fiel SB, eds. Seminars in Respiratory and Critical Care Medicine: Vol. 15; Cystic Fibrosis. New York and Stuttgart, Thieme Medical Publishers, 1994; pp. 383-390.
-
(1994)
Seminars in Respiratory and Critical Care Medicine: Vol. 15; Cystic Fibrosis
, vol.15
, pp. 383-390
-
-
Burke, W.1
Aitken, M.L.2
-
4
-
-
0027395872
-
The changing epidemiology of cystic fibrosis
-
FitzSimmons SC. The changing epidemiology of cystic fibrosis. Pediatr 1993; 122: 1-9.
-
(1993)
Pediatr
, vol.122
, pp. 1-9
-
-
Fitzsimmons, S.C.1
-
5
-
-
0026523829
-
Cystic fibrosis: Molecular biology and therapeutic implications
-
Collins FS. Cystic fibrosis: molecular biology and therapeutic implications. Science 1992; 256: 774-779.
-
(1992)
Science
, vol.256
, pp. 774-779
-
-
Collins, F.S.1
-
6
-
-
0004775961
-
A scoring system for short-term evaluation of patients with cystsic fibrosis: A possible means for assessment of antibiotic efficacy
-
Warwick WJ, ed. Minnesota University of Minnesota Dept of Pediatrics Medical School in cooperation with International Cystic Fibrosis Association National Heart Lung and Blood Institute and Fogarty International Center
-
Huang N, Helen HK, Palmer J, Hsuan F. A scoring system for short-term evaluation of patients with cystsic fibrosis: a possible means for assessment of antibiotic efficacy. In: Warwick WJ, ed. 1,000 years of Cystic Fibrosis Collected Papers, Minnesota University of Minnesota Dept of Pediatrics Medical School in cooperation with International Cystic Fibrosis Association National Heart Lung and Blood Institute and Fogarty International Center, 1981; pp. 207-215.
-
(1981)
1,000 Years of Cystic Fibrosis Collected Papers
, pp. 207-215
-
-
Huang, N.1
Helen, H.K.2
Palmer, J.3
Hsuan, F.4
-
7
-
-
0030928550
-
Internal consistency reliability and predictive validity of a modified N. Huang clinical scoring system in adult cystic fibrosis patients
-
Matouk E, Ghezzo RH, Gruber J, Hidvegi R, Gray-Donald K. Internal consistency reliability and predictive validity of a modified N. Huang clinical scoring system in adult cystic fibrosis patients. Eur Respir J 1997; 10: 2004-2013.
-
(1997)
Eur Respir J
, vol.10
, pp. 2004-2013
-
-
Matouk, E.1
Ghezzo, R.H.2
Gruber, J.3
Hidvegi, R.4
Gray-Donald, K.5
-
8
-
-
0030795172
-
A systematic overview of the measurement properties of the chronic respiratory questionnaire
-
Lacasse Y, Wong E, Guyatt G. A systematic overview of the measurement properties of the chronic respiratory questionnaire. Can Respir J 1997; 4: 131-139.
-
(1997)
Can Respir J
, vol.4
, pp. 131-139
-
-
Lacasse, Y.1
Wong, E.2
Guyatt, G.3
-
9
-
-
0027481874
-
Measuring health-related quality of life
-
Guyatt G, Feeny DH. Measuring health-related quality of life. Ann Intern Med 1993; 118: 622-629.
-
(1993)
Ann Intern Med
, vol.118
, pp. 622-629
-
-
Guyatt, G.1
Feeny, D.H.2
-
10
-
-
0023442646
-
Standardization of spirometry 1987 update
-
American Thoracic Society. Standardization of spirometry 1987 update. Am Rev Respir Dis 1987; 136: 1285-1295.
-
(1987)
Am Rev Respir Dis
, vol.136
, pp. 1285-1295
-
-
-
11
-
-
0020585150
-
Changes in the normal maximal expiratory flow-volume curve with growth and aging
-
Knudson RJ, Lebowitz MD, Holberg CJ, Burrows B. Changes in the normal maximal expiratory flow-volume curve with growth and aging. Am Rev Respir Dis 1983; 127: 725-734.
-
(1983)
Am Rev Respir Dis
, vol.127
, pp. 725-734
-
-
Knudson, R.J.1
Lebowitz, M.D.2
Holberg, C.J.3
Burrows, B.4
-
12
-
-
0019241461
-
Comparison of lung function and survival patterns between cystic fibrosis and emphysema or chronic bronchitis patients
-
Sturgess JM, ed. Perspectives in Cystic Fibrosis Mississauga, Ontario, Imperial Press
-
Wagener JS, Taussig LM, Burrows B, Hernried L, Boat T. Comparison of lung function and survival patterns between cystic fibrosis and emphysema or chronic bronchitis patients. In: Sturgess JM, ed. Perspectives in Cystic Fibrosis. Proceedings of the 8th International Cystic Fibrosis Congress. Mississauga, Ontario, Imperial Press, 1980; pp. 236-245.
-
(1980)
Proceedings of the 8th International Cystic Fibrosis Congress
, pp. 236-245
-
-
Wagener, J.S.1
Taussig, L.M.2
Burrows, B.3
Hernried, L.4
Boat, T.5
-
14
-
-
0023639146
-
Clinical features, survival rate and prognostic factors in young adults with cystic fibrosis
-
Huang NN, Schidlow D, Szatrowski T, et al. Clinical features, survival rate and prognostic factors in young adults with cystic fibrosis. Am J Med 1987; 82: 871-879.
-
(1987)
Am J Med
, vol.82
, pp. 871-879
-
-
Huang, N.N.1
Schidlow, D.2
Szatrowski, T.3
-
15
-
-
0025355607
-
Pulmonary function and clinical course in patients with cystic fibrosis after pulmonary colonization with Pseudomonas aeruginosa
-
Kerem E, Corey M, Gold R, Levision H. Pulmonary function and clinical course in patients with cystic fibrosis after pulmonary colonization with Pseudomonas aeruginosa. J Pediatr 1990; 116: 714-719.
-
(1990)
J Pediatr
, vol.116
, pp. 714-719
-
-
Kerem, E.1
Corey, M.2
Gold, R.3
Levision, H.4
-
16
-
-
0029016495
-
Gender differences in cystic fibrosis: Pseudomonas aeruginosa infection
-
Demko CA, Byard PJ, Davis PB. Gender differences in cystic fibrosis: Pseudomonas aeruginosa infection. J Clin Epidemiol 1995; 48: 1041-1049.
-
(1995)
J Clin Epidemiol
, vol.48
, pp. 1041-1049
-
-
Demko, C.A.1
Byard, P.J.2
Davis, P.B.3
-
17
-
-
0027227670
-
Emergence of antibiotics resistance amongst Pseudomonas aeruginosa isolates from patients with cystic fibrosis
-
Mouton JW, Den-Hollander JG, Horrevorts AM. Emergence of antibiotics resistance amongst Pseudomonas aeruginosa isolates from patients with cystic fibrosis. J Antimicrob Chemother 1993; 31: 919-926.
-
(1993)
J Antimicrob Chemother
, vol.31
, pp. 919-926
-
-
Mouton, J.W.1
Den-Hollander, J.G.2
Horrevorts, A.M.3
-
18
-
-
0024985943
-
Variability of pulmonary function tests of lung in cystic fibrosis
-
Cooper P, Robertson C, Hudson I, Phelan P. Variability of pulmonary function tests of lung in cystic fibrosis. Pediatr Pulmonol 1990; 8: 16-22.
-
(1990)
Pediatr Pulmonol
, vol.8
, pp. 16-22
-
-
Cooper, P.1
Robertson, C.2
Hudson, I.3
Phelan, P.4
-
19
-
-
0026667228
-
Validating the SF-36 health survey questionnaire: New outcome measure for primary care
-
Brazier JE, Harper R, Jones NMB, et al. Validating the SF-36 health survey questionnaire: new outcome measure for primary care. BMJ 1992; 305: 160-164.
-
(1992)
BMJ
, vol.305
, pp. 160-164
-
-
Brazier, J.E.1
Harper, R.2
Jones, N.M.B.3
-
20
-
-
0021982047
-
A methodological framework for assessing health indices
-
Kirshner B, Guyatt G. A methodological framework for assessing health indices. J Chron Dis 1985; 38: 27-36.
-
(1985)
J Chron Dis
, vol.38
, pp. 27-36
-
-
Kirshner, B.1
Guyatt, G.2
-
21
-
-
0027327877
-
The relationship between tests of lung function and three chest radiological scoring systems in patients with cystic fibrosis
-
Wong EB, Regnis J, Shier RC, Bye PT, Stewart ME. The relationship between tests of lung function and three chest radiological scoring systems in patients with cystic fibrosis. Austras Radiol 1993; 37: 265-269.
-
(1993)
Austras Radiol
, vol.37
, pp. 265-269
-
-
Wong, E.B.1
Regnis, J.2
Shier, R.C.3
Bye, P.T.4
Stewart, M.E.5
-
22
-
-
0028136443
-
The chest radiograph in cystic fibrosis: A new scoring system compared with the Chrispin-Norman and Brasfield scores
-
Conway SP, Pond MN, Bowler I, et al. The chest radiograph in cystic fibrosis: a new scoring system compared with the Chrispin-Norman and Brasfield scores. Thorax 1994; 49: 860-862.
-
(1994)
Thorax
, vol.49
, pp. 860-862
-
-
Conway, S.P.1
Pond, M.N.2
Bowler, I.3
-
23
-
-
0027965872
-
Critical evaluation of three radiograph scores in cystic fibrosis
-
Sawyer SM, Carlin JB, DeCampo M, Bowes G. Critical evaluation of three radiograph scores in cystic fibrosis. Thorax 1994; 49: 866-863.
-
(1994)
Thorax
, vol.49
, pp. 866-1863
-
-
Sawyer, S.M.1
Carlin, J.B.2
DeCampo, M.3
Bowes, G.4
-
24
-
-
0026504803
-
Spirometry and chest roengenographic appearance in adults with cystic fibrosis
-
Rosenberg SM, Howatt WF, Grum CM. Spirometry and chest roengenographic appearance in adults with cystic fibrosis. Chest 1992; 101: 961-964.
-
(1992)
Chest
, vol.101
, pp. 961-964
-
-
Rosenberg, S.M.1
Howatt, W.F.2
Grum, C.M.3
-
26
-
-
0014037416
-
Measurement of pulmonary function in cystic fibrosis
-
Rossi E, Stoll E, eds. New York, S Krager AG
-
Matthews IW, Doershuk CF. Measurement of pulmonary function in cystic fibrosis. In: Rossi E, Stoll E, eds. Modem Problems in Pediatrics. Vol 10. New York, S Krager AG, 1967; p. 237.
-
(1967)
Modem Problems in Pediatrics
, vol.10
, pp. 237
-
-
Matthews, I.W.1
Doershuk, C.F.2
-
27
-
-
0015043620
-
Pulmonary function and response to exercise in children with cystic fibrosis
-
Godfrey S, Mearns M. Pulmonary function and response to exercise in children with cystic fibrosis. Arch Dis Child 1971; 46: 144-157.
-
(1971)
Arch Dis Child
, vol.46
, pp. 144-157
-
-
Godfrey, S.1
Mearns, M.2
-
28
-
-
0014883478
-
Dynamic and static lung volumes, blood gas tensions and diffusing capacity in patients with cystic fibrosis
-
Featherby FA, Weng T-R, Crozier DN, Duic A, Reilly BJ, Levison H. Dynamic and static lung volumes, blood gas tensions and diffusing capacity in patients with cystic fibrosis. Am Rev Respir Dis 1970; 102: 737-749.
-
(1970)
Am Rev Respir Dis
, vol.102
, pp. 737-749
-
-
Featherby, F.A.1
Weng, T.-R.2
Crozier, D.N.3
Duic, A.4
Reilly, B.J.5
Levison, H.6
-
29
-
-
0344834574
-
Mortality and progression of the NIH clinical and prognostic score
-
Abstract
-
Wielinski CL, Warwick WJ, Budd JR. Mortality and progression of the NIH clinical and prognostic score. Pediatric Pulmonol 1990; 16: Suppl. 5, 259-260. (Abstract).
-
(1990)
Pediatric Pulmonol
, vol.16
, Issue.SUPPL. 5
, pp. 259-260
-
-
Wielinski, C.L.1
Warwick, W.J.2
Budd, J.R.3
-
30
-
-
0021834116
-
How should we measure function in patients with chronic heart and lung disease?
-
Guyatt GH, Thompson PJ, Berman LB, et al. How should we measure function in patients with chronic heart and lung disease? J Chron Dis 1985; 38: 517-524.
-
(1985)
J Chron Dis
, vol.38
, pp. 517-524
-
-
Guyatt, G.H.1
Thompson, P.J.2
Berman, L.B.3
-
31
-
-
0028210008
-
Factor analysis of exercise capacity, dyspnoea ratings and lung function in patients with severe COPD
-
Wegener RE, Jorres RA, Kirsten DK, Magnussen H. Factor analysis of exercise capacity, dyspnoea ratings and lung function in patients with severe COPD. Eur Respir J 1994; 7: 725-729.
-
(1994)
Eur Respir J
, vol.7
, pp. 725-729
-
-
Wegener, R.E.1
Jorres, R.A.2
Kirsten, D.K.3
Magnussen, H.4
-
32
-
-
0028362805
-
Relation of lung function, maximal inspiratory pressure, dyspnea and quality of life with exercise capacity in paients with chronic obstructive pulmonary disease
-
Wijkistra PJ, Ten Vergert EM, van der Mark TW, et al. Relation of lung function, maximal inspiratory pressure, dyspnea and quality of life with exercise capacity in paients with chronic obstructive pulmonary disease. Thorax 1994; 49: 468-472.
-
(1994)
Thorax
, vol.49
, pp. 468-472
-
-
Wijkistra, P.J.1
Ten Vergert, E.M.2
Van Der Mark, T.W.3
|