4,5-Dimethyl-3-hydroxy-2[5H]-furanone (sotolone) - The odour of maple syrup urine disease

Journal of Inherited Metabolic Disease

Volumn 22, Issue 2, 1999, Pages 107-114

  Podebrad, F ^a   Heil, M ^a   Reichert, S ^a   Mosandl, A ^a   Sewell, A C ^a   Bohles H ^a  

^a GOETHE UNIVERSITY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

2 OXOACID DEHYDROGENASE; FURANONE DERIVATIVE;

ARTICLE; CHEMICAL STRUCTURE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; GAS CHROMATOGRAPHY; HUMAN; MAPLE SYRUP URINE DISEASE; MASS SPECTROMETRY; NORMAL HUMAN; URINALYSIS;

FURANS; HUMANS; MAPLE SYRUP URINE DISEASE; MOLECULAR STRUCTURE; ODORS;

EID: 0032898293     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005433516026     Document Type: Article

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