G(M2)-ganglioside metabolism in situ in mucolipidosis IV fibroblasts

Neurochemical Research

Volumn 24, Issue 4, 1999, Pages 475-479

  Raghavan, S ^a   Leshinsky, E ^a   Kolodny, E H ^a  

^a NEW YORK UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Ganglioside metabolism; Ganglioside neuraminidase; Mucolipidosis IV

Indexed keywords

CHOLESTEROL; GANGLIOSIDE GM2; HYDROLASE; LYSOSOME ENZYME; PHOSPHORUS; SIALIDASE;

ARTICLE; CONTROLLED STUDY; FIBROBLAST; HUMAN; HUMAN CELL; HYDROLYSIS; LIPID METABOLISM; LYSOSOME STORAGE DISEASE; MUCOLIPIDOSIS; PRIORITY JOURNAL; RADIOACTIVITY;

EID: 0032892829     PISSN: 03643190     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1022523527283     Document Type: Article

References (40)

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