Erythropoietic protoporphyria with fatal liver failure

Journal of Gastroenterology

Volumn 34, Issue 3, 1999, Pages 405-409

  Ishibashi, Akiko ^a   Ogata, Riko ^a   Sakisaka, Shotaro ^a   Kumashiro, Ryukichi ^a   Koga, Yuriko ^a   Mitsuyama, Keiichi ^a   Kuromatsu, Ryoko ^a   Uchimura, Yasuyo ^a   Ijyuin, Hiroyasu ^a   Tanaka, Kumi ^a   Iwao, Tadashi ^a   Ishii, Kunihide ^a   Sata, Michio ^a   Inoue, Yoshiko ^a   Kin, Yasuko ^a   Oizumi, Kotaro ^a   Nishida, Hidemi ^a   Imaizumi, Tsutomu ^a   Tanikawa, Kyuichi ^b  

^a KURUME UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b International Institute for Liver Research   (Japan)

Author keywords

Erythropoietic protoporphyria; Liver failure; Treatment

Indexed keywords

BETA CAROTENE; COLESTYRAMINE; COPROPORPHYRIN; PORPHYRIN; PROTOPORPHYRIN;

ABDOMINAL PAIN; ADULT; ARTICLE; CASE REPORT; CLINICAL FEATURE; ERYTHROCYTE; ERYTHROCYTE TRANSFUSION; ERYTHROPOIETIC PROTOPORPHYRIA; ESOPHAGUS VARICES BLEEDING; FEMALE; HEMODIALYSIS; HUMAN; HUMAN CELL; HUMAN TISSUE; INTRAHEPATIC BILE DUCT; LIVER BIOPSY; LIVER CELL; LIVER CIRRHOSIS; LIVER DYSFUNCTION; LIVER FAILURE; LIVER FUNCTION; MULTIPLE ORGAN FAILURE; PHOTOSENSITIVITY; PRIORITY JOURNAL;

ADULT; AUTOPSY; BIOPSY, NEEDLE; DISEASE PROGRESSION; DRUG THERAPY, COMBINATION; ESOPHAGEAL AND GASTRIC VARICES; FATAL OUTCOME; FEMALE; HUMANS; LIVER CIRRHOSIS; LIVER FAILURE; LIVER FUNCTION TESTS; MULTIPLE ORGAN FAILURE; PORPHYRIA, HEPATOERYTHROPOIETIC; RENAL DIALYSIS; RUPTURE, SPONTANEOUS;

EID: 0032806627     PISSN: 09441174     EISSN: None     Source Type: Journal    
DOI: 10.1007/s005350050284     Document Type: Article

References (17)

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