Synthesis of mevalonate pathway lipids in fibroblasts from Zellweger and X-linked ALD patients

Pediatric Research

Volumn 46, Issue 3, 1999, Pages 345-350

  Appelkvist, Eeva Liisa ^a   Venizelos, Nikolaos ^b   Zhang, Yiyi ^a   Parmryd, Ingela ^c   Hagenfeldt, Lars ^b   Dallner, Gustav ^c  

^a Clinical Research Center   (Sweden)

^b KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

^c STOCKHOLM UNIVERSITY   (Sweden)

Author keywords

[No Author keywords available]

Indexed keywords

CHOLESTEROL; DOLICHOL; GERANYLTRANSFERASE; LIPID; MEVALONIC ACID; SQUALENE SYNTHASE; UBIQUINONE;

ADRENOLEUKODYSTROPHY; ARTICLE; CELLULAR DISTRIBUTION; CHOLESTEROL SYNTHESIS; CONTROLLED STUDY; ENZYME ACTIVITY; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; LIPOGENESIS; PEROXISOME; PRIORITY JOURNAL; QUANTITATIVE ASSAY; REACTION TIME; TISSUE DISTRIBUTION; X CHROMOSOME LINKED DISORDER; ZELLWEGER SYNDROME;

EID: 0032774480     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/00006450-199909000-00017     Document Type: Article

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