Intracellular localization of the Menkes and Wilson's disease proteins and their role in intracellular copper transport

Pediatrics International

Volumn 41, Issue 4, 1999, Pages 436-442

  Suzuki, Mariko ^a   Gitlin, Jonathan D ^b  

^a TOHO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

ATP7A; ATP7B; Copper metabolism; Menkes disease; Post Golgi vesicular compartment; Trans Golgi network; Wilson disease

Indexed keywords

ADENOSINE TRIPHOSPHATASE; COPPER; COPPER DERIVATIVE; HISTIDINE COPPER; ISOENZYME; PENICILLAMINE; UNCLASSIFIED DRUG;

CELLULAR DISTRIBUTION; CLINICAL FEATURE; COPPER METABOLISM; GENE ISOLATION; GOLGI COMPLEX; HUMAN; INTRACELLULAR TRANSPORT; MENKES SYNDROME; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; REVIEW; SUBCUTANEOUS DRUG ADMINISTRATION; TISSUE DISTRIBUTION; WILSON DISEASE;

EID: 0032769249     PISSN: 13288067     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1442-200x.1999.01090.x     Document Type: Review

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