Plasma concentrations and renal clearance of orotic acid in argininosuccinic acid synthetase deficiency

Pediatric Nephrology

Volumn 13, Issue 9, 1999, Pages 912-916

  Sass, Jörn Oliver ^a   Skladal, Daniela ^a  

^a Univ Klin F Kinder Jugendheilkunde   (Austria)

Author keywords

Amino acid; Argininosuccinic acid; Citrullinemia; Orotic acid; Pyrimidine metabolism; Renal clearance

Indexed keywords

AMMONIA; ARGININOSUCCINATE SYNTHASE; GLUTAMINE; OROTIC ACID; PYRIMIDINE;

AMINO ACID BLOOD LEVEL; AMMONIA BLOOD LEVEL; ARTICLE; BLOOD LEVEL; CASE REPORT; CITRULLINEMIA; GLOMERULUS FILTRATION RATE; HUMAN; INFANT; KIDNEY CLEARANCE; MALE; NEWBORN; PATHOGENESIS; PATIENT MONITORING; PRESCHOOL CHILD; PRIORITY JOURNAL; PYRIMIDINE METABOLISM;

EID: 0032763034     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004670050726     Document Type: Article

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