Concomitant administration of sodium dichloroacetate and thiamine in West syndrome caused by thiamine-responsive pyruvate dehydrogenase complex deficiency

Journal of the Neurological Sciences

Volumn 171, Issue 1, 1999, Pages 56-59

  Naito, Etsuo ^a   Ito, Michinori ^a   Yokota, Ichiro ^a   Saijo, Takahiko ^a   Chen, Shuli ^a   Maehara, Mitsuo ^b   Kuroda, Yasuhiro ^a  

^a UNIVERSITY OF TOKUSHIMA   (Japan)

^b CHUBU NATIONAL HOSPITAL   (Japan)

Author keywords

Congenital lactic acidemia; High dose thiamine, Thiamine responsive pyruvate dehydrogenase deficiency; Sodium dichloroacetate; West syndrome

Indexed keywords

DICHLOROACETIC ACID; THIAMINE;

ARTICLE; CASE REPORT; FEMALE; HUMAN; INFANT; LACTIC ACIDOSIS; PRESCHOOL CHILD; PRIORITY JOURNAL; PYRUVATE DEHYDROGENASE COMPLEX DEFICIENCY; WEST SYNDROME;

EID: 0032741902     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-510X(99)00250-6     Document Type: Article

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