Liver transplantation in maple syrup urine disease

European Journal of Pediatrics, Supplement

Volumn 158, Issue 2, 1999, Pages

  Wendel, U ^a   Saudubray, J M ^b   Bodner, A ^a   Schadewaldt, P ^a  

^a HEINRICH HEINE UNIVERSITY   (Germany)

^b HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

Branched chain amino acids; Liver transplantation; Maple syrup urine disease; Metabolism; Stable isotopes

Indexed keywords

BRANCHED CHAIN AMINO ACID;

ARTICLE; AUTOSOMAL RECESSIVE DISORDER; COMPLEX FORMATION; DIETARY INTAKE; ENZYME ACTIVITY; HUMAN; INTELLECT; LIVER TRANSPLANTATION; MAPLE SYRUP URINE DISEASE; METABOLIC REGULATION; PRIORITY JOURNAL; PROTEIN RESTRICTION; PROTEIN SYNTHESIS INHIBITION;

AMINO ACIDS; CHILD; CHILD, PRESCHOOL; DIET, PROTEIN-RESTRICTED; FEMALE; HUMANS; LIVER TRANSPLANTATION; MALE; MAPLE SYRUP URINE DISEASE; RISK FACTORS;

EID: 0032731258     PISSN: 09439676     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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