Malonic aciduria in Maltese dogs: Normal methylmalonic acid concentrations and malonyl-CoA decarboxylase activity in fibroblasts

Journal of Inherited Metabolic Disease

Volumn 22, Issue 8, 1999, Pages 883-890

  O'Brien, D P ^a   Barshop, B A ^c   Faunt, K K ^a   Johnson, G C ^b   Gibson, K M ^e   Shelton, G D ^d  

^a UNIVERSITY OF MISSOURI   (United States)

^b UNIVERSITY OF MISSOURI   (United States)

^c UNIVERSITY OF CALIFORNIA SAN DIEGO   (United States)

^d UNIVERSITY OF CALIFORNIA   (United States)

^e OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CARBOXYLIC ACID; CARBOXYLYASE; CYANOCOBALAMIN; DEXPANTHENOL; KETONE BODY; MALONIC ACID; MALONYL COENZYME A; MEDIUM CHAIN TRIACYLGLYCEROL; METHYLMALONIC ACID; NICOTINAMIDE; PYRIDOXINE; RIBOFLAVIN; THIAMINE; VITAMIN B COMPLEX;

ACIDOSIS; ACIDURIA; ANIMAL CELL; ARTICLE; CAUSE OF DEATH; CONTROLLED STUDY; DOG; ENZYME ACTIVITY; FAMILY; FEMALE; FIBROBLAST; HUMAN; HUMAN CELL; HYPOGLYCEMIA; KETONURIA; LOW FAT DIET; MALTA; METABOLIC DISORDER; NEUROLOGIC DISEASE; NONHUMAN; SEIZURE; STUPOR; URINE LEVEL;

ANIMALS; CARBOXY-LYASES; DIET; DOG DISEASES; DOGS; EPILEPSY, TONIC-CLONIC; FEMALE; FIBROBLASTS; MALONATES; METABOLISM, INBORN ERRORS; METHYLMALONIC ACID; PEDIGREE;

EID: 0032712124     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005635306257     Document Type: Article

References (14)

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