Absence of the α6(IV) chain of collagen type IV in alport syndrome is related to a failure at the protein assembly level and does not result in diffuse leiomyomatosis

American Journal of Pathology

Volumn 154, Issue 6, 1999, Pages 1883-1891

  Zheng, Keqin ^a   Harvey, Scott ^a   Sado, Yoshikazu ^b   Naito, Ichiro ^b   Ninomiya, Yoshifumi ^c   Jacobs, Robert ^d   Thorner, Paul S ^a  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b Shigei Medical Research Institute   (Japan)

^c OKAYAMA UNIVERSITY MEDICAL SCHOOL   (Japan)

^d UNIVERSITY OF GUELPH   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN TYPE 4; COLLAGEN; MESSENGER RNA;

ALPORT SYNDROME; ARTICLE; CONTROLLED STUDY; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; LEIOMYOMATOSIS; NORTHERN BLOTTING; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DETERMINATION; RNA ANALYSIS; X CHROMOSOME LINKED DISORDER; ANIMAL; BLADDER; DNA SEQUENCE; DOG; GENETICS; MALE; METABOLISM; MOLECULAR CLONING; MOLECULAR GENETICS; NEPHRITIS; NUCLEOTIDE SEQUENCE; PROMOTER REGION; SEQUENCE HOMOLOGY; SMOOTH MUSCLE;

ANIMALS; BASE SEQUENCE; BLOTTING, NORTHERN; CLONING, MOLECULAR; COLLAGEN; DOGS; HUMANS; IMMUNOHISTOCHEMISTRY; LEIOMYOMATOSIS; MALE; MOLECULAR SEQUENCE DATA; MUSCLE, SMOOTH; NEPHRITIS, HEREDITARY; PROMOTER REGIONS (GENETICS); RNA, MESSENGER; SEQUENCE ANALYSIS, DNA; SEQUENCE HOMOLOGY, NUCLEIC ACID; URINARY BLADDER;

EID: 0032587805     PISSN: 00029440     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0002-9440(10)65446-6     Document Type: Article

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47. American Journal of Pathology, Vol. 154, No. 6, June 1999