Abnormality in catalase import into peroxisomes leads to severe neurological disorder

Proceedings of the National Academy of Sciences of the United States of America

Volumn 95, Issue 6, 1998, Pages 2961-2966

  Sheikh, Faruk G ^a   Pahan, Kalipada ^a   Khan, Mushfiquddin ^a   Barbosa, Ernest ^a   Singh, Inderjit ^a  

^a MEDICAL UNIVERSITY OF SOUTH CAROLINA   (United States)

Author keywords

Peroxisomal disease; Peroxisomal targeting signal

Indexed keywords

AMINOTRIAZOLE; CATALASE; DIHYDROXYACETONE PHOSPHATE ACYLTRANSFERASE; FATTY ACID; HYDROGEN PEROXIDE; LIGNOCERIC ACID; PHYTANIC ACID; PLASMALOGEN; REACTIVE OXYGEN METABOLITE;

ARTICLE; CELL CULTURE; CELLULAR DISTRIBUTION; CHIMERA; ENZYME INACTIVATION; ENZYME LOCALIZATION; FIBROBLAST; GENE TARGETING; HUMAN; HUMAN CELL; NEUROLOGIC DISEASE; PEROXISOME; PRIORITY JOURNAL;

ANIMALS; BIOLOGICAL TRANSPORT; CATALASE; CELL COMPARTMENTATION; CELL LINE; FATTY ACIDS; FIBROBLASTS; HUMANS; HYDROGEN PEROXIDE; MICROBODIES; NERVOUS SYSTEM DISEASES; PEROXISOMAL DISORDERS; PLASMALOGENS; PROTEIN SORTING SIGNALS; RECEPTORS, CYTOPLASMIC AND NUCLEAR; ZELLWEGER SYNDROME;

EID: 0032539803     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.95.6.2961     Document Type: Article

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