Phenylketonuria: The in vivo hydroxylation rate of phenylalanine into tyrosine is decreased

Journal of Clinical Investigation

Volumn 101, Issue 12, 1998, Pages 2875-2880

  Van Spronsen, F J ^a   Reijngoud, D J ^a   Smit, G P A ^a   Nagel, G T ^b   Stellaard, F ^a   Berger, R ^c   Heymans, H S A ^d  

^a UNIVERSITY OF GRONINGEN   (Netherlands)

^b UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^c UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^d UNIVERSITY OF AMSTERDAM   (Netherlands)

Author keywords

Diet; L 1 13C tyrosine; L ring 2H4 tyrosine; L ring 2H5 phenylalanine

Indexed keywords

PHENYLALANINE; PHENYLALANINE 4 MONOOXYGENASE; TYROSINE;

ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; ENZYME DEFICIENCY; HUMAN; HYDROXYLATION; PHENYLKETONURIA; PRIORITY JOURNAL;

EID: 0032525820     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI737     Document Type: Article

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