Gene-dose effect on carnitine transport activity in embryonic fibroblasts of JVS mice as a model of human carnitine transporter deficiency

Biochemical Pharmacology

Volumn 55, Issue 10, 1998, Pages 1729-1732

  Hashimoto, Noriyoshi ^a   Suzuki, Fumio ^c   Tamai, Ikumi ^b   Nikaido, Hiroko ^a   Kuwajima, Masamichi ^d   Hayakawa, Jun Ichiro ^a   Tsuji, Akira ^b  

^a KANAZAWA UNIV SCHOOL OF MEDICINE   (Japan)

^b KANAZAWA UNIVERSITY   (Japan)

^c HIROSHIMA UNIVERSITY   (Japan)

^d UNIVERSITY OF TOKUSHIMA   (Japan)

Author keywords

Embryonic fibroblast; JVS mouse; Membrane transporter; Systemic carnitine deficiency; Uptake kinetics

Indexed keywords

CARNITINE; CARRIER PROTEIN;

AMINO ACID BLOOD LEVEL; AMINO ACID TRANSPORT; ANIMAL CELL; ANIMAL MODEL; ARTICLE; BINDING AFFINITY; CARNITINE DEFICIENCY; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; FEMALE; FIBROBLAST; HOMOZYGOSITY; MALE; MICHAELIS CONSTANT; MOUSE; NONHUMAN; PRIORITY JOURNAL; STEATOSIS; STEREOSPECIFICITY; TEMPERATURE;

ANIMALS; BIOLOGICAL TRANSPORT; CARNITINE; CARRIER PROTEINS; DISEASE MODELS, ANIMAL; EMBRYO; FIBROBLASTS; GENE DOSAGE; HETEROZYGOTE; HOMOZYGOTE; HUMANS; KINETICS; LIPID METABOLISM, INBORN ERRORS; MICE; MICE, MUTANT STRAINS;

EID: 0032525016     PISSN: 00062952     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0006-2952(97)00670-9     Document Type: Article

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