The Tight skin mouse: Demonstration of mutant fibrillin-1 production and assembly into abnormal microfibrils

Journal of Cell Biology

Volumn 140, Issue 5, 1998, Pages 1159-1166

  Kielty, Cay M ^a   Raghunath, Michael ^b   Siracusa, Linda D ^c   Sherratt, Michael J ^a   Peters, Reiner ^b,c   Shuttleworth, C Adrian ^a   Jimenez, Sergio A ^c  

^a UNIVERSITY OF MANCHESTER   (United Kingdom)

^b UNIVERSITY OF MÜNSTER   (Germany)

^c THOMAS JEFFERSON UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FIBRILLIN;

ANIMAL CELL; ARTICLE; CELL ULTRASTRUCTURE; GENE DUPLICATION; GENE MUTATION; IMMUNOHISTOCHEMISTRY; MOUSE; NONHUMAN; PERIODICITY; POLYMERIZATION; PRIORITY JOURNAL; PROTEIN ASSEMBLY; SCANNING ELECTRON MICROSCOPY; SKIN FIBROBLAST; TRANSMISSION ELECTRON MICROSCOPY;

ANIMALS; CHELATING AGENTS; CONNECTIVE TISSUE; EDETIC ACID; FIBROBLASTS; GUANIDINES; LEUKOCYTE ELASTASE; MICE; MICE, INBRED C57BL; MICROFILAMENT PROTEINS; MICROSCOPY, CONFOCAL; MICROSCOPY, ELECTRON; MUTATION; SKIN; TRYPSIN;

ANIMALIA;

EID: 0032498849     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.140.5.1159     Document Type: Article

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